CONCURRENT SICKLE-CELL-ANEMIA AND ALPHA-THALASSEMIA - EFFECT ON PATHOLOGICAL PROPERTIES OF SICKLE ERYTHROCYTES

被引:121
作者
EMBURY, SH [1 ]
CLARK, MR [1 ]
MONROY, G [1 ]
MOHANDAS, N [1 ]
机构
[1] UNIV CALIF SAN FRANCISCO, NO CALIF COMPRENS SICKLE CELL CTR, DEPT LAB MED, SAN FRANCISCO, CA 94110 USA
关键词
D O I
10.1172/JCI111181
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:116 / 123
页数:8
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共 57 条
[41]  
LUX SE, 1977, BLOOD, V50, P625
[42]   IRREVERSIBLE DEFORMATION OF SPECTRIN-ACTIN LATTICE IN IRREVERSIBLY SICKLED CELLS [J].
LUX, SE ;
JOHN, KM ;
KARNOVSKY, MJ .
JOURNAL OF CLINICAL INVESTIGATION, 1976, 58 (04) :955-963
[43]   NUCLEOTIDE-SEQUENCE OF RIGHTWARD OPERATOR OF PHAGE LAMBDA [J].
MANIATIS, T ;
JEFFREY, A ;
KLEID, DG .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1975, 72 (03) :1184-1188
[44]  
MEARS JG, 1983, BLOOD, V62, P286
[45]  
MILLER RG, 1981, SIMULTANEOUS STATIST, P90
[46]   ANALYSIS OF FACTORS REGULATING ERYTHROCYTE DEFORMABILITY [J].
MOHANDAS, N ;
CLARK, MR ;
JACOBS, MS ;
SHOHET, SB .
JOURNAL OF CLINICAL INVESTIGATION, 1980, 66 (03) :563-573
[47]   DETERMINATION OF DEOXYHEMOGLOBIN-S POLYMER IN SICKLE ERYTHROCYTES UPON DEOXYGENATION [J].
NOGUCHI, CT ;
TORCHIA, DA ;
SCHECHTER, AN .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1980, 77 (09) :5487-5491
[48]   INTRACELLULAR POLYMERIZATION OF SICKLE HEMOGLOBIN - EFFECTS OF CELL HETEROGENEITY [J].
NOGUCHI, CT ;
TORCHIA, DA ;
SCHECHTER, AN .
JOURNAL OF CLINICAL INVESTIGATION, 1983, 72 (03) :846-852
[49]   INTERACTION OF PHOSPHATIDYLSERINE-PHOSPHATIDYLCHOLINE LIPOSOMES WITH SICKLE ERYTHROCYTES - EVIDENCE FOR ALTERED MEMBRANE-SURFACE PROPERTIES [J].
SCHWARTZ, RS ;
DUZGUNES, N ;
CHIU, DTY ;
LUBIN, B .
JOURNAL OF CLINICAL INVESTIGATION, 1983, 71 (06) :1570-1580
[50]  
SERJEANT GR, 1975, CLIN HAEMATOL, V4, P109