THE DIAGNOSIS AND ASSESSMENT OF AN ADULT WITH ANOMALOUS ORIGIN OF THE LEFT CORONARY-ARTERY FROM THE PULMONARY-ARTERY

被引:0
作者
COWIE, MR
MAHMOOD, S
ELL, PJ
机构
[1] WHITTINGTON HOSP, DEPT CARDIAC, LONDON N19 5NF, ENGLAND
[2] UCL, SCH MED, INST NUCL MED, LONDON W1N 8AA, ENGLAND
来源
EUROPEAN JOURNAL OF NUCLEAR MEDICINE | 1994年 / 21卷 / 09期
关键词
BLAND-WHITE-GARLAND SYNDROME; TL-201; SINGLE-PHOTON EMISSION TOMOGRAPHY; CONGENITAL HEART DISEASE;
D O I
暂无
中图分类号
R8 [特种医学]; R445 [影像诊断学];
学科分类号
1002 ; 100207 ; 1009 ;
摘要
Anomalous origin of the left coronary artery from the pulmonary artery (the Bland-White-Garland syndrome) is a rare congenital cardiac defect which may present for the first time in adulthood. The recognition of this disorder, which produces widespread left ventricular ischaemia and the risk of sudden death, myocardial infarction and congestive heart failure, is important as the prognosis can be improved by surgical intervention. Thallium-201 scintigraphy has a useful role in demonstrating the widespread nature of the ischaemia of the left ventricle, whilst the diagnosis is confirmed at car diac catheterisation.
引用
收藏
页码:1017 / 1019
页数:3
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