SYNTHESIS AND MATURATION OF CROSS-REACTIVE GLYCOPROTEIN IN FIBROBLASTS DEFICIENT IN ARYLSULFATASE A ACTIVITY

被引:39
作者
BACH, G [1 ]
NEUFELD, EF [1 ]
机构
[1] NIADDKD, GENET & BIOCHEM BRANCH, BETHESDA, MD 20205 USA
关键词
D O I
10.1016/0006-291X(83)91816-8
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:198 / 205
页数:8
相关论文
共 27 条
[1]   FILM DETECTION METHOD FOR TRITIUM-LABELED PROTEINS AND NUCLEIC-ACIDS IN POLYACRYLAMIDE GELS [J].
BONNER, WM ;
LASKEY, RA .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1974, 46 (01) :83-88
[2]   MOLECULAR DEFECT IN COMBINED BETA-GALACTOSIDASE AND NEURAMINIDASE DEFICIENCY IN MAN [J].
DAZZO, A ;
HOOGEVEEN, A ;
REUSER, AJJ ;
ROBINSON, D ;
GALJAARD, H .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (15) :4535-4539
[3]  
Fluharty A L, 1978, Methods Enzymol, V50, P537
[4]   CEREBROSIDE SULFATE HYDROLYSIS BY FIBROBLASTS FROM A PARENT WITH METACHROMATIC LEUKODYSTROPHY [J].
FLUHARTY, AL ;
STEVENS, RL ;
KIHARA, H .
JOURNAL OF PEDIATRICS, 1978, 92 (05) :782-784
[5]   PSEUDO ARYLSULFATASE A DEFICIENCY - EVIDENCE FOR A STRUCTURALLY ALTERED ENZYME [J].
FLUHARTY, AL ;
MEEK, WE ;
KIHARA, H .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1983, 112 (01) :191-197
[6]  
FLUHARTY AL, 1978, AM J HUM GENET, V30, P249
[7]  
FLUHARTY AL, 1978, T AM SOC NEUROCHEM, V9, P163
[8]   CHLOROQUINE INHIBITS LYSOSOMAL-ENZYME PINOCYTOSIS AND ENHANCES LYSOSOMAL ENZYME-SECRETION BY IMPAIRING RECEPTOR RECYCLING [J].
GONZALEZNORIEGA, A ;
GRUBB, JH ;
TALKAD, V ;
SLY, WS .
JOURNAL OF CELL BIOLOGY, 1980, 85 (03) :839-852
[9]  
Hall C W, 1978, Methods Enzymol, V50, P439
[10]  
HASILIK A, 1980, J BIOL CHEM, V255, P4946