POLYSPLENIA SYNDROME - A CASE ASSOCIATED WITH TRANSHEPATIC PORTAL-VEIN, SHORT PANCREAS, AND LEFT INFERIOR VENA-CAVA WITH HEMIAZYGOUS CONTINUATION

被引:34
作者
SENER, RN
ALPER, H
机构
[1] Department of Radiology, Ege University Hospital, Bornova, TR-35100, Izmir
来源
ABDOMINAL IMAGING | 1994年 / 19卷 / 01期
关键词
SPLEEN; ABNORMALITIES; CT; PORTAL VEIN; VENA CAVA; PANCREAS; POLYSPLENIA SYNDROME;
D O I
10.1007/BF02165866
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
This paper presents a 57-year-old asymptomatic patient with the polysplenia syndrome with abdominal manifestations. In addition to multiple spleens, the abdominal findings included a left inferior vena cava with hemiazygous continuation, a striking portal anomaly with the portal vein following an ''intraperitoneal-left transhepatic'' route to reach the porta hepatis, and a congenitally short pancreas.
引用
收藏
页码:64 / 66
页数:3
相关论文
共 7 条
[1]   BILIARY ATRESIA AND NONCARDIAC POLYSPLENIC SYNDROME - US AND SURGICAL CONSIDERATIONS [J].
ABRAMSON, SJ ;
BERDON, WE ;
ALTMAN, RP ;
AMODIO, JB ;
LEVY, J .
RADIOLOGY, 1987, 163 (02) :377-379
[2]   POLYSPLENIA AND JEJUNAL ATRESIA WITH AGENESIS OF THE DORSAL MESENTERY [J].
BARBER, GA ;
WHALEN, TV ;
MOORE, G .
JOURNAL OF PEDIATRIC SURGERY, 1989, 24 (11) :1161-1161
[3]  
BOYER B, 1987, Journal de Radiologie (Paris), V68, P285
[4]  
HADAR H, 1991, ACTA RADIOL, V32, P299
[5]  
Hatayama C, 1984, Pediatr Pathol, V2, P127
[6]   POLYSPLENIA SYNDROME WITH CONGENITAL SHORT PANCREAS [J].
HERMAN, TE ;
SIEGEL, MJ .
AMERICAN JOURNAL OF ROENTGENOLOGY, 1991, 156 (04) :799-800
[7]   VISCEROATRIAL SITUS ABNORMALITIES - SONOGRAPHIC AND COMPUTED TOMOGRAPHIC APPEARANCE [J].
TONKIN, ILD ;
TONKIN, AK .
AMERICAN JOURNAL OF ROENTGENOLOGY, 1982, 138 (03) :509-515