ACCUMULATION OF 3-HYDROXYISOBUTYRIC ACID, 2-METHYL-3-HYDROXYBUTYRIC ACID AND 3-HYDROXYISOVALERIC ACID IN KETOACIDOSIS

被引:87
作者
LANDAAS, S [1 ]
机构
[1] UNIV OSLO,RIKS HOSP,INST CLIN BIOCHEM,OSLO 1,NORWAY
关键词
D O I
10.1016/0009-8981(75)90196-5
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
摘要
引用
收藏
页码:143 / 154
页数:12
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[1]   Studies on the physiology of the liver XV. Effect of total removal of the liver on deaminization [J].
Bollman, JL ;
Mann, FC ;
Magath, TB .
AMERICAN JOURNAL OF PHYSIOLOGY, 1926, 78 (02) :258-269
[2]  
BURCH RE, 1961, J BIOL CHEM, V239, P4111
[3]  
CAHILL GF, 1970, ADIPOSE TISSUE REGUL, P181
[4]  
DAUM RS, 1971, LANCET, V2, P1289
[5]   INHERITED DISORDER OF ISOLEUCINE CATABOLISM CAUSING ACCUMULATION OF ALPHA-METHYLACETOACETATE AND ALPHA-METHYL-BETA-HYDROXYBUTYRATE, AND INTERMITTENT METABOLIC-ACIDOSIS [J].
DAUM, RS ;
SCRIVER, CR ;
MAMER, OA ;
DELVIN, E ;
LAMM, P ;
GOLDMAN, H .
PEDIATRIC RESEARCH, 1973, 7 (03) :149-160
[6]   POSSIBILITY OF INBORN DEFECT IN ISOVALERICACIDEMIA INVOLVING ALTERED ENZYME SPECIFICITY RATHER THAN TOTAL INACTIVITY [J].
ENGEL, PC .
NATURE, 1974, 248 (5444) :140-142
[7]   PLASMA AMINO ACID LEVELS IN DIABETIC KETOACIDOSIS [J].
FELIG, P ;
MARLISS, E ;
OHMAN, JL ;
CAHILL, GF .
DIABETES, 1970, 19 (10) :727-&
[8]  
FRITZ IB, 1974, REGULATION HEPATIC M, P224
[9]  
Garland P B, 1968, Adv Enzyme Regul, V6, P3, DOI 10.1016/0065-2571(68)90005-8
[10]  
GOEBELL H, 1964, BIOCHEM Z, V340, P441