INHIBITION OF BRAIN GLUTAMATE DECARBOXYLASE BY GLUTARATE, GLUTACONATE, AND BETA-HYDROXYGLUTARATE - EXPLANATION OF SYMPTOMS IN GLUTARIC ACIDURIA

被引:88
作者
STOKKE, O [1 ]
GOODMAN, SI [1 ]
MOE, PG [1 ]
机构
[1] UNIV COLORADO,MED CTR,DEPT PEDIAT,4200 E 9TH AVE,DENVER,CO 80220
关键词
D O I
10.1016/0009-8981(76)90241-2
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
摘要
引用
收藏
页码:411 / 415
页数:5
相关论文
共 16 条
[1]  
BAXTER CF, 1970, HDB NEUROCHEMISTRY, V3, P289
[2]  
BIRD ED, 1973, LANCET, V1, P1090
[3]   HUNTINGTONS-CHOREA - POSTMORTEM MEASUREMENT OF GLUTAMIC-ACID DECARBOXYLASE, CHOLINE-ACETYLTRANSFERASE AND DOPAMINE IN BASAL GANGLIA [J].
BIRD, ED ;
IVERSEN, LL .
BRAIN, 1974, 97 (SEP) :457-472
[4]   VERTEILUNG VON NORADRENALIN UND DOPAMIN (3-HYDROXYTYRAMIN) IM GEHIRN DES MENSCHEN UND IHR VERHALTEN BEI ERKRANKUNGEN DES EXTRAPYRAMIDALEN SYSTEMS [J].
EHRINGER, H ;
HORNYKIEWICZ, O .
KLINISCHE WOCHENSCHRIFT, 1960, 38 (24) :1236-1239
[5]   GLUTARIC ACIDURIA - NEW DISORDER OF AMINO-ACID METABOLISM [J].
GOODMAN, SI ;
MARKEY, SP ;
MOE, PG ;
MILES, BS ;
TENG, CC .
BIOCHEMICAL MEDICINE, 1975, 12 (01) :12-21
[6]   GLUTARIC ACIDURIA - INHERITED DEFICIENCY OF GLUTARYL-COA DEHYDROGENASE-ACTIVITY [J].
GOODMAN, SI ;
KOHLHOFF, JG .
BIOCHEMICAL MEDICINE, 1975, 13 (02) :138-140
[7]   AN ANION STIMULATED L-GLUTAMIC ACID DECARBOXYLASE IN NON-NEURAL TISSUES - OCCURRENCE AND SUBCELLULAR LOCALIZATION IN MOUSE KIDNEY AND DEVELOPING CHICK EMBRYO BRAIN [J].
HABER, B ;
KURIYAMA, K ;
ROBERTS, E .
BIOCHEMICAL PHARMACOLOGY, 1970, 19 :1119-&
[8]  
KRAVITZ EA, 1967, NEUROSCIENCES, P433
[9]  
LOWRY OH, 1951, J BIOL CHEM, V193, P265
[10]   CHOLINE ACETYLASE AND GLUTAMIC-ACID DECARBOXYLASE IN HUNTINGTONS-CHOREA - PRELIMINARY STUDY [J].
MCGEER, PL ;
MCGEER, EG ;
FIBIGER, HC .
NEUROLOGY, 1973, 23 (09) :912-917