METABOLISM OF 3-ALPHA, 7-ALPHA, 12-ALPHA-TRIHYDROXY-5-BETA-CHOLESTAN-26-OIC ACID IN 2 SIBLINGS WITH CHOLESTASIS DUE TO INTRAHEPATIC BILE-DUCT ANOMALIES - APPARENT INBORN ERROR OF CHOLIC ACID SYNTHESIS

被引：111
作者：
HANSON, RF
NEVINISENBERG, J
WILLIAMS, GC
HACHEY, D
SZCZEPANIK, P
KLEIN, PD
SHARP, HL
机构：
[1] ARGONNE NATL LAB, DIV BIOL & MED RES, ARGONNE, IL 60439 USA
[2] UNIV MINNESOTA HOSP, DEPT PEDIAT, MINNEAPOLIS, MN 55455 USA
[3] UNIV MINNESOTA HOSP, DEPT INTERN MED, GASTROENTEROL UNITS, MINNEAPOLIS, MN 55455 USA
来源：
JOURNAL OF CLINICAL INVESTIGATION | 1975年 / 56卷 / 03期
关键词：
D O I：
10.1172/JCI108127
中图分类号：
R-3 [医学研究方法]; R3 [基础医学];
学科分类号：
1001 ;
摘要：
引用
收藏
页码：577 / 587
页数：11
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