DEFECTIVE B-CELLS IN ATAXIA-TELANGIECTASIA, AND HETEROGENEITY OF COMMON VARIABLE IMMUNODEFICIENCY

被引:0
作者
SAKIYAMA, Y [1 ]
ARIGA, T [1 ]
HASHIMOTO, F [1 ]
MATSUMOTO, S [1 ]
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[1] HOKKAIDO UNIV,SCH MED,DEPT PEDIAT,SAPPORO,HOKKAIDO 060,JAPAN
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Q [生物科学];
学科分类号
07 ; 0710 ; 09 ;
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页码:A7 / A7
页数:1
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[21]   CHROMOSOME CHANGES CONNECT IMMUNODEFICIENCY AND CANCER IN ATAXIA-TELANGIECTASIA [J].
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