PERIODONTAL MANIFESTATION OF HYPOPHOSPHATASIA - A FAMILY CASE-REPORT

被引:21
作者
PLAGMANN, HC [1 ]
KOCHER, T [1 ]
KUHRAU, N [1 ]
CALIEBE, A [1 ]
机构
[1] INST HUMAN GENET & ANTHROPOL,D-24105 KIEL,GERMANY
关键词
HYPOPHOSPHATASIA; PREMATURE DECIDUOUS TOOTH LOSS; ODONTOHYPOPHOSPHATASIA;
D O I
10.1111/j.1600-051X.1994.tb00791.x
中图分类号
R78 [口腔科学];
学科分类号
1003 ;
摘要
Hypophosphatasia is a rare inherited disease, the 1st clinical sign of which is often a premature loss of deciduous teeth. We describe clinical, histological and SEM findings of 2 cases of hypophosphatasia from a single family and discuss the pathological mechanisms with reference to the literature.
引用
收藏
页码:710 / 716
页数:7
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