PROGRESSIVE MULTIFOCAL LEUKOENCEPHALOPATHY COMPLICATING WISKOTT-ALDRICH SYNDROME - REPORT OF A CASE AND REVIEW OF THE LITERATURE OF PROGRESSIVE MULTIFOCAL LEUKOENCEPHALOPATHY WITH OTHER INHERITED IMMUNODEFICIENCY STATES

被引:37
作者
KATZ, DA
BERGER, JR
HAMILTON, B
MAJOR, EO
POST, JD
机构
[1] UNIV MIAMI,SCH MED,DEPT NEUROL,MIAMI,FL 33136
[2] UNIV MIAMI,SCH MED,DEPT PEDIAT,MIAMI,FL 33136
[3] UNIV MIAMI,SCH MED,DEPT INTERNAL MED,MIAMI,FL 33136
[4] UNIV MIAMI,SCH MED,DEPT MICROBIOL & IMMUNOL,MIAMI,FL 33136
[5] UNIV MIAMI,SCH MED,DEPT RADIOL,MIAMI,FL 33136
[6] NINCDS,VIRAL & MOLEC PATHOGENESIS LAB,BETHESDA,MD 20892
关键词
D O I
10.1001/archneur.1994.00540160128016
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Objective: To describe the occurrence of progressive multifocal leukoencephalopathy (PML) in association with Wiskott-Aldrich syndrome, an X-linked recessive disorder with impairment of both cellular and humoral immunity. Design: A detailed analysis of this patient's clinical illness, immunologic factors, neuroradiographic findings, and brain histopathologic condition was undertaken. The medical literature on PML complicating congenital immunodeficient states was also reviewed. Setting: A 1500-bed, university-affiliated, public health hospital.
引用
收藏
页码:422 / 426
页数:5
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