Neonatal Bartter Syndrome: A Newborn Case

被引:0
|
作者
Ozdemir, Ozmert Muhammet Ali [1 ]
Kucuktasci, Kazim [1 ]
Ozdemir, Emine [2 ]
Urey, Turgut [1 ]
Ergin, Hacer [1 ]
Evrengul, Havva [3 ]
机构
[1] Pamukkale Univ, Tip Fak, Neonatol Bilim Dali, Denizli, Turkey
[2] Pamukkale Univ, Tip Fak, Cocuk Sagligi & Hastaliklari Anabilim Dali, Denizli, Turkey
[3] Pamukkale Univ, Tip Fak, Cocuk Nefrol Bilim Dali, Denizli, Turkey
关键词
Neonatal Bartter syndrome; hypokalemia; hypochloremia; metabolic alkalosis; indomethacin;
D O I
10.4274/jpr.14633
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Neonatal Bartter syndrome (BS) is an inherited renal tubular disorder characterized with normal blood pressure, hypokalemia, hypochloremic metabolic alkalosis, hyperreninemia and increased urinary loss of sodium, potassium and chloride. In this disorder complications such as severe dehydration episodes, recurrent vomiting, hypercalciuria, and subsequently nephrocalcinosis, growth and development retardations. Herein, we reported a premature infant with neonatal BS, who successfully treated by oral indomethacin and potassium supplements without any complications.
引用
收藏
页码:89 / 91
页数:3
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