Neonatal Bartter Syndrome: A Newborn Case

被引:0
|
作者
Ozdemir, Ozmert Muhammet Ali [1 ]
Kucuktasci, Kazim [1 ]
Ozdemir, Emine [2 ]
Urey, Turgut [1 ]
Ergin, Hacer [1 ]
Evrengul, Havva [3 ]
机构
[1] Pamukkale Univ, Tip Fak, Neonatol Bilim Dali, Denizli, Turkey
[2] Pamukkale Univ, Tip Fak, Cocuk Sagligi & Hastaliklari Anabilim Dali, Denizli, Turkey
[3] Pamukkale Univ, Tip Fak, Cocuk Nefrol Bilim Dali, Denizli, Turkey
关键词
Neonatal Bartter syndrome; hypokalemia; hypochloremia; metabolic alkalosis; indomethacin;
D O I
10.4274/jpr.14633
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Neonatal Bartter syndrome (BS) is an inherited renal tubular disorder characterized with normal blood pressure, hypokalemia, hypochloremic metabolic alkalosis, hyperreninemia and increased urinary loss of sodium, potassium and chloride. In this disorder complications such as severe dehydration episodes, recurrent vomiting, hypercalciuria, and subsequently nephrocalcinosis, growth and development retardations. Herein, we reported a premature infant with neonatal BS, who successfully treated by oral indomethacin and potassium supplements without any complications.
引用
收藏
页码:89 / 91
页数:3
相关论文
共 50 条
  • [11] Polyhydramnios and high urea levels as leading signs of neonatal Bartter syndrome: a case report
    Ermler, C.
    Marx-Berger, D.
    Laux, R.
    SWISS MEDICAL WEEKLY, 2011, 141 : 33S - 33S
  • [12] Neonatal Bartter syndrome with cholelithiasis and hydrocephalus: Rare association
    Ozdemir, Ozmert M. A.
    Cirali, Ceren
    Agladioglu, Sebahat Yilmaz
    Evrengul, Havva
    Tepeli, Emre
    Ergin, Hacer
    PEDIATRICS INTERNATIONAL, 2016, 58 (09) : 912 - 915
  • [13] BARTTER SYNDROME IN 2 SIBLINGS - ANTENATAL AND NEONATAL OBSERVATIONS
    PROESMANS, W
    DEVLIEGER, H
    VANASSCHE, A
    EGGERMONT, E
    VANDENBERGHE, K
    LEMMENS, F
    SIEPRATH, P
    LIJNEN, P
    INTERNATIONAL JOURNAL OF PEDIATRIC NEPHROLOGY, 1985, 6 (01): : 63 - 70
  • [14] Acetyl salicylic acid treatment in neonatal Bartter syndrome
    Suna Şerife Oğuz
    Tülin Gökmen
    Ömer Erdeve
    Nurdan Uras
    Ugur Dilmen
    Pediatric Nephrology, 2011, 26 : 1339 - 1340
  • [15] Indomethacin for renal impairment in neonatal Bartter's syndrome
    Craig, JC
    Falk, MC
    LANCET, 1996, 347 (9000): : 550 - 550
  • [16] Acetyl salicylic acid treatment in neonatal Bartter syndrome
    Oguz, Suna Serife
    Gokmen, Tulin
    Erdeve, Omer
    Uras, Nurdan
    Dilmen, Ugur
    PEDIATRIC NEPHROLOGY, 2011, 26 (08) : 1339 - 1340
  • [17] ANTENATAL AND NEONATAL OBSERVATIONS IN A PATIENT WITH BARTTER SYNDROME (BS)
    PROESMANS, W
    LEMMENS, F
    DEVLIEGER, H
    VANASSCHE, A
    INTERNATIONAL JOURNAL OF PEDIATRIC NEPHROLOGY, 1984, 5 (02): : 112 - 113
  • [18] An extreme example of the neonatal form of Bartter's syndrome
    Williams, MP
    Jones, CL
    Johnstone, LM
    Walker, RG
    McCredie, DA
    Powell, HR
    PEDIATRIC NEPHROLOGY, 1996, 10 (04) : 496 - 497
  • [20] Classical Bartter syndrome - A case report
    Mali, Lalit Prakash
    Meena, Shyam Sundar
    Baniwal, Mukesh
    INDIAN JOURNAL OF MEDICAL SPECIALITIES, 2015, 6 (03) : 116 - 118