MULTIPLE ISOELECTRIC AND RECOGNITION FORMS OF HUMAN BETA-GLUCURONIDASE ACTIVITY

被引：62
作者：
GLASER, JH
ROOZEN, KJ
BROT, FE
SLY, WS
机构：
[1] WASHINGTON UNIV,SCH MED,DEPT PEDIAT,ST LOUIS,MO 63130
[2] ST LOUIS CHILDRENS HOSP,DIV MED GENET,ST LOUIS,MO 63110
[3] ST LOUIS CHILDRENS HOSP,DEPT PEDIAT,500 S KINGS HIGHWAY,ST LOUIS,MO 63110
来源：
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS | 1975年 / 166卷 / 02期
关键词：
D O I：
10.1016/0003-9861(75)90417-8
中图分类号：
Q5 [生物化学]; Q7 [分子生物学];
学科分类号：
071010 ; 081704 ;
摘要：
引用
收藏
页码：536 / 542
页数：7
相关论文
共 16 条
[1]   IN-VITRO CORRECTION OF DEFICIENT HUMAN FIBROBLASTS BY BETA-GLUCURONIDASE FROM DIFFERENT HUMAN SOURCES [J].
BROT, FE ;
GLASER, JH ;
ROOZEN, KJ ;
SLY, WS .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1974, 57 (01) :1-8
[2]  
DAVIS BJ, 1962, DISC ELECTROPHORESIS
[3]   ELECTROPHORETIC SEPARATION OF MULTIPLE BANDS WITH BETA-GLUCURONIDASE ACTIVITY IN HUMAN SERA [J].
FONDO, EY ;
BARTALOS, M .
BIOCHEMICAL GENETICS, 1969, 3 (06) :591-&
[4]  
GLASER JH, 1973, J LAB CLIN MED, V82, P969
[5]   GENETIC-HETEROGENEITY IN MULTIPLE LYSOSOMAL HYDROLASE DEFICIENCY [J].
GLASER, JH ;
MCALISTER, WH ;
SLY, WS .
JOURNAL OF PEDIATRICS, 1974, 85 (02) :192-198
[6]   BETA-GLUCURONIDASE DEFICIENCY MUCOPOLYSACCHARIDOSIS - STUDIES IN CULTURED FIBROBLASTS [J].
HALL, CW ;
CANTZ, M ;
NEUFELD, EF .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1973, 155 (01) :32-38
[7]   HYPOTHESIS FOR I-CELL DISEASE - DEFECTIVE HYDROLASES THAT DO NOT ENTER LYSOSOMES [J].
HICKMAN, S ;
NEUFELD, EF .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1972, 49 (04) :992-&
[8]   RECOGNITION MARKER REQUIRED FOR UPTAKE OF A LYSOSOMAL ENZYME BY CULTURED FIBROBLASTS [J].
HICKMAN, S ;
SHAPIRO, LJ ;
NEUFELD, EF .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1974, 57 (01) :55-61
[9]   MUCOPOLYSACCHARIDOSIS - SECONDARILY INDUCED ABNORMAL DISTRIBUTION OF LYSOSOMAL ISOENZYMES [J].
KINT, JA ;
DACREMONT, G ;
CARTON, D ;
ORYE, E ;
HOOFT, C .
SCIENCE, 1973, 181 (4097) :352-354
[10]   ACID PHOSPHATASES FROM DIFFERENT ORGANS AND ANIMAL FORMS COMPARED BY STARCH-GEL ELECTROPHOREIS [J].
LUNDIN, LG ;
ALLISON, AC .
ACTA CHEMICA SCANDINAVICA, 1966, 20 (09) :2579-+
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