EFFECT OF PROPIONIC-ACID ON FATTY-ACID OXIDATION AND UREAGENESIS

被引:60
作者
GLASGOW, AM [1 ]
CHASE, HP [1 ]
机构
[1] UNIV COLORADO,MED CTR,BF STOLINSKY LABS,DENVER,CO 80220
关键词
D O I
10.1203/00006450-197610070-00010
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:683 / 686
页数:4
相关论文
共 18 条
[1]   PROPIONIC ACIDEMIA IN PATIENTS WITH KETOTIC HYPERGLYCINEMIA [J].
ANDO, T ;
RASMUSSEN, K ;
NYHAN, WL ;
DONNELL, GN ;
BARNES, ND .
JOURNAL OF PEDIATRICS, 1971, 78 (05) :827-+
[2]  
COHEN PP, 1957, MANOMETRIC TECHNIQUE, P149
[3]   STUDIES ON HYPOGLYCEMIC COMPOUND CYCLOPROPANECARBOXYLIC ACID - EFFECTS ON FATTY-ACID OXIDATION IN-VITRO [J].
DUNCOMBE, WG ;
RISING, TJ .
BIOCHEMICAL PHARMACOLOGY, 1972, 21 (08) :1075-&
[4]   PRODUCTION OF FEATURES OF REYES SYNDROME IN RATS WITH 4-PENTENOIC ACID [J].
GLASGOW, AM ;
CHASE, HP .
PEDIATRIC RESEARCH, 1975, 9 (03) :133-138
[5]  
GLASGOW AM, IN PRESS
[6]   BIOCHEMICAL EFFECTS OF HYPOGLYCEMIC COMPOUND PENT-4-ENOIC ACID AND RELATED NON-HYPOGLYCEMIC FATTY-ACIDS - EFFECTS OF FREE ACIDS AND THEIR CARNITINE ESTERS ON COENZYME-A-DEPENDENT OXIDATIONS IN RAT-LIVER MITOCHONDRIA [J].
HOLLAND, PC ;
SHERRATT, HS .
BIOCHEMICAL JOURNAL, 1973, 136 (01) :157-171
[7]   BIOCHEMICAL EFFECTS OF HYPOGLYCEMIC COMPOUND PENT-4-ENOIC ACID AND RELATED NON-HYPOGLYCEMIC FATTY-ACIDS - EFFECTS OF THEIR COENZYME-A ESTERS ON ENZYMES OF FATTY-ACID OXIDATION [J].
HOLLAND, PC ;
SENIOR, AE ;
SHERRATT, HS .
BIOCHEMICAL JOURNAL, 1973, 136 (01) :173-184
[8]   PROPIONICACIDEMIA A NEW INBORN ERROR OF METABOLISM [J].
HOMMES, FA ;
KUIPERS, JRG ;
ELEMA, JD ;
JANSEN, JF ;
JONXIS, JHP .
PEDIATRIC RESEARCH, 1968, 2 (06) :519-&
[9]  
LOWRY OH, 1951, J BIOL CHEM, V193, P265
[10]  
MAMUNES P, 1974, PEDIATR RES, V8, P436, DOI 10.1203/00006450-197404000-00573