Total hip arthroplasty in Hurler syndrome - 8 years follow up - A case report with review of literature

被引：2

作者：

Gautam, Deepak ^{[1
]}

Malhotra, Rajesh ^{[1
]}

机构：

[1] All India Inst Med Sci, Dept Orthoped, New Delhi 110029, India

来源：

JOURNAL OF ORTHOPAEDICS | 2018年 / 15卷 / 01期

基金：

英国惠康基金;

关键词：

Mucopolysaccharidosis; Hurler syndrome; Total hip arthroplasty;

D O I：

10.1016/j.jor.2018.01.036

中图分类号：

R826.8 [整形外科学]; R782.2 [口腔颌面部整形外科学]; R726.2 [小儿整形外科学]; R62 [整形外科学（修复外科学）];

学科分类号：

摘要：

Life expectancy in Hurler syndrome is significantly improved by enzyme therapy with bone marrow transplantation. However, the deterioration of skeletal abnormalities persists. Hip dysplasia is a common presentation which may progress to significant hip arthritis requiring total hip arthroplasty at later stage. We report a long-term outcome of cementless total hip arthroplasty in a patient with Hurler syndrome who was successfully treated with bone marrow transplant.

引用

页码：111 / 113

页数：3

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