Williams-Campbell syndrome: a case report

被引:6
作者
Konoglou, Maria [1 ]
Porpodis, Konstantinos [2 ]
Zarogoulidis, Paul [2 ]
Loridas, Nikolaos [1 ]
Katsikogiannis, Nikolaos [3 ]
Mitrakas, Alexandros [2 ]
Zervas, Vasilis [2 ]
Kontakiotis, Theodoros [2 ]
Papakosta, Despoina [2 ]
Boglou, Panagiotis [4 ]
Bakali, Stamatia [5 ]
Courcoutsakis, Nikolaos [6 ]
Zarogoulidis, Konstantinos [2 ]
机构
[1] G Papanikolaou Gen Hosp, Pulm Clin 1, Thessaloniki, Greece
[2] Aristotle Univ Thessaloniki, G Papanikolaou Gen Hosp, Pulm Dept, Thessaloniki, Greece
[3] Univ Gen Hosp Alexandroupolis, Surg Dept NHS, Thessaloniki, Greece
[4] Democritus Univ Thrace, Univ Gen Hosp Alexandroupolis, Pulm Dept, Thrace, Greece
[5] Democritus Univ Thrace, Univ Gen Hosp Alexandroupolis, Microbiol Dept, Thessaloniki, Greece
[6] Democritus Univ Thrace, Univ Gen Hosp Alexandroupolis, Radiol Dept, Thessaloniki, Greece
关键词
bronchietasis; Williams-Campbell syndrome; bronchomalacia;
D O I
10.2147/IJGM.S28447
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Introduction: Williams-Campbell syndrome, also known as bronchomalacia, is a rare -disorder characterized by a deficiency of cartilage in subsegmental bronchi, leading to distal airway collapse and bronchiectasis. There have been few reports about patients affected by saccular bronchiectasis, paracicatricial emphysema, and diminished cartilage. These are all characteristic of Williams-Campbell syndrome. Case presentation: This report presents a 57-year-old woman with progressive dyspnea, cough, sputum production, and fever. The clinical and laboratory examination revealed that the patient had a respiratory infection due to bronchiectasis caused by Williams-Campbell syndrome, which was undiagnosed in the patient until then. Conclusion: Although a rare syndrome, when patients' signs and symptoms include recurrent respiratory infections, bronchiectasis, productive cough, and dyspnea, Williams-Campbell syndrome should be included in the differential diagnosis.
引用
收藏
页码:41 / 44
页数:4
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