We describe a case of an extralobar pulmonary sequestration diagnosed prenatally via ultrasound. The lesion was followed serially during pregnancy and then thoracoscopically resected when the infant was 5 months old. A preoperative computed tomography (CT) scan with contrast demonstrated a single arterial vessel from the aorta, yet intraoperatively, three separate systemic arteries were identified. Pulmonary sequestration is a rare congenital malformation of the lung in which anatomic variants are the rule rather than the exception. This unique case is an example of such and emphasizes the importance of constant vigilance for aberrant anatomy during resection. Published by Elsevier Inc. Open access under CC BY-NC-ND license.