MALIGNANT PERIPHERAL-NERVE SHEATH TUMOR ARISING IN A DENOVO GANGLIONEUROMA - A CASE-REPORT

被引:17
作者
DAMIANI, S
MANETTO, V
CARRILLO, G
DIBLASI, A
NAPPI, O
EUSEBI, V
机构
[1] CARDARELLI HOSP,DEPT ANAT PATHOL,NAPLES,ITALY
[2] G RUMMO HOSP,DEPT ANAT PATHOL,BENEVENTO,ITALY
关键词
D O I
10.1177/030089169107700121
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
A case of a << de novo >> ganglioneuroma showing an internal area of malignant nerve sheath tumor is described. The tumor arose in an 18-year-old girl without a history of von Reckling-hausen's disease. Immunohistochemically, the ganglioneuromatous component was positive with anti-synaptophysin, anti-S100 protein and anti-vimentin antisera, whereas the malignant part was immunoreactive only with anti-S100 protein and anti-vimentin antisera. The patient is free of disease 4 years after surgery. The clinicopathologic features of this rare case are discussed.
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页码:90 / 93
页数:4
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