Brugada syndrome in children

被引:7
作者
Crosson, Jane E. [1 ]
Nies, Melanie [1 ]
机构
[1] Johns Hopkins Univ Hosp, Pediat Cardiol Bloomberg Childrens Ctr, 1800 Orleans St, Baltimore, MD 21287 USA
关键词
Brugada syndrome; children; defibrillator; ECG; genetic syndrome; quinidine; SCN5A; ST elevation; sudden death; ventricular tachycardia;
D O I
10.1586/14779072.2015.999765
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Brugada syndrome is an inherited arrhythmia associated with characteristic ST elevation in the right precordial leads and sudden cardiac death. The average age of sudden cardiac death is 40 years; reported pediatric cases remain rare. Genetic testing and increased disease awareness may result in many more children being diagnosed with Brugada syndrome.
引用
收藏
页码:173 / 181
页数:9
相关论文
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