Angiosarcoma of the scalp associated with Xeroderma pigmentosum

被引:9
作者
Sharma, Shilpi [1 ]
Deshmukh, Anuja D. [1 ]
Bal, Munita M. [2 ]
Chaukar, Devendra A. [1 ]
Dcruz, Anil K. [1 ]
机构
[1] Tata Mem Hosp, Dept Head & Neck Surg Oncol, Mumbai 400012, Maharashtra, India
[2] Tata Mem Hosp, Dept Pathol, Mumbai, Maharashtra, India
关键词
Angiosarcoma; genodermatosis; Xeroderma pigmentosum;
D O I
10.4103/0971-5851.99753
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
Xeroderma pigmentosum (XP) is a rare autosomal recessive genodermatosis associated with hypersensitivity to ultraviolet light due to defects in Deoxyribonucleic acid (DNA) repair. These patients have more than a 1000-fold increased risk of developing skin cancers. Although multiple cutaneous malignancies are common, the simultaneous occurrence of angiosarcoma and basal cell carcinoma is a rare phenomenon. We report a case of a 25-year-old male with XP with angiosarcoma scalp and basal cell carcinoma of face and occiput and discuss the treatment of this aggressive neoplasm with a review of the literature pertaining to it.
引用
收藏
页码:126 / 129
页数:4
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