PRIMITIVE POLYPOID ANTIGRANULOCYTES-CELL TUMOR AND OTHER CUTANEOUS ANTIGRANULOCYTES-CELL NEOPLASMS OF APPARENT NONNEURAL ORIGIN

被引:125
作者
LEBOIT, PE
BARR, RJ
BURALL, S
METCALF, JS
YEN, TSB
WICK, MR
机构
[1] UNIV CALIF SAN FRANCISCO,DEPT DERMATOL,SAN FRANCISCO,CA 94143
[2] UNIV CALIF IRVINE,DEPT DERMATOL,IRVINE,CA 92717
[3] UNIV CALIF IRVINE,DEPT PATHOL,IRVINE,CA 92717
[4] KAISER PERMANENTE MED CTR,DEPT PATHOL,SAN FRANCISCO,CA
[5] MED UNIV S CAROLINA,DEPT PATHOL,CHARLESTON,SC 29425
[6] MED UNIV S CAROLINA,DEPT DERMATOL,CHARLESTON,SC 29425
[7] WASHINGTON UNIV,BARNES HOSP,SCH MED,DIV SURG PATHOL,ST LOUIS,MO 63110
关键词
SKIN; ANTIGRANULOCYTES-CELL TUMOR; BASAL-CELL CARCINOMA; LEIOMYOSARCOMA;
D O I
10.1097/00000478-199101000-00006
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
Most cutaneous and noncutaneous granular-cell tumors are currently thought to be of Schwann-cell derivation. We present seven unusual cutaneous granular-cell lesions in which Schwann-cell origin can be excluded or is inapparent. Four of these lesions are of a previously undescribed type, and, unlike conventional granular-cell tumors of the skin, show a polypoid configuration, numerous mitoses, cytologic atypia, and a primitive immunophenotype. We propose the term "primitive polypoid granular-cell tumor" for these lesions. One occurred in a child, and three in adults. There have been no metastases to date, with follow-up periods of 2, 4, 4, and 16 years, respectively, although one tumor recurred locally. Additional cases and longer follow-up may be required to rule out the possibility that primitive polypoid granular-cell tumor is a low-grade malignancy. Two other granular-cell lesions represent variants of leiomyosarcoma, one of which widely metastasized. The last case is a granular-cell form of nodular basal-cell carcinoma. Cutaneous granular-cell neoplasms can show varying differentiation and behaviour. Pathologists should not equate the occurrence of cytoplasmic granularity in a cutaneous neoplasm with the diagnosis of granular-cell schwannoma.
引用
收藏
页码:48 / 58
页数:11
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