INFLAMMATORY FAMILIAL PALMOPLANTAR KERATODERMA - GREITHERS DISEASE

被引:12
作者
BEYLOTBARRY, M [1 ]
TAIEB, A [1 ]
SURLEVEBAZEILLE, JE [1 ]
MALEVILLE, J [1 ]
机构
[1] HOP ENFANTS,SERV DERMATOL,F-33077 BORDEAUX,FRANCE
关键词
PALMOPLANTAR KERATODERMA; ELECTRON MICROSCOPY; CHILD;
D O I
10.1159/000247449
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
A case of a familial palmoplantar inflammatory keratoderma with autosomal dominant inheritance is reported. Associated clinical features included vasomotor troubles and hyperhidrosis consistent with a diagnosis of Greither's disease. Light microscopy was nonspecific. Electron microscopy showed aggregated tonofilaments around the nucleus, without true clumps. Desmosomes were numerous and cell-cell junctions showed an imbricated pattern, well demonstrated in the stratum corneum. The diagnosis of Greither's keratoderma is discussed.
引用
收藏
页码:210 / 214
页数:5
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