MOLECULAR AND CELL BIOLOGY OF CYSTIC-FIBROSIS

被引：5

作者：

DAVIS, PB

机构：

来源：

JOURNAL OF APPLIED PHYSIOLOGY | 1991年 / 70卷 / 05期

关键词：

D O I：

10.1152/jappl.1991.70.5.2331

中图分类号：

Q4 [生理学];

学科分类号：

071003 ;

摘要：

引用

页码：2331 / 2333

页数：3

共 12 条

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[2] DEFECTIVE INTRACELLULAR-TRANSPORT AND PROCESSING OF CFTR IS THE MOLECULAR-BASIS OF MOST CYSTIC-FIBROSIS [J].

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[3] ALTERED REGULATION OF AIRWAY EPITHELIAL-CELL CHLORIDE CHANNELS IN CYSTIC-FIBROSIS [J].

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[5] EXPRESSION OF THE CYSTIC-FIBROSIS GENE IN NONEPITHELIAL INVERTEBRATE CELLS PRODUCES A REGULATED ANION CONDUCTANCE [J].

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HANRAHAN, JW ;

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SUN, SZ ;

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[6] IDENTIFICATION OF THE CYSTIC-FIBROSIS GENE - GENETIC-ANALYSIS [J].

KEREM, BS ;

ROMMENS, JM ;

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MARKIEWICZ, D ;

COX, TK ;

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TSUI, LC .

SCIENCE, 1989, 245 (4922) :1073-1080

[7] THE RELATION BETWEEN GENOTYPE AND PHENOTYPE IN CYSTIC-FIBROSIS - ANALYSIS OF THE MOST COMMON MUTATION (DELTA-F508) [J].

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[8] CYCLIC AMP-DEPENDENT PROTEIN-KINASE OPENS CHLORIDE CHANNELS IN NORMAL BUT NOT CYSTIC-FIBROSIS AIRWAY EPITHELIUM [J].

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[9]

QUINTON PM, 1989, CLIN CHEM, V35, P726

[10]

RIORDAN JR, 1989, SCIENCE, V245, P1066

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