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GLUTARYL-COA DEHYDROGENASE-ACTIVITY DETERMINED WITH INTACT ELECTRON-TRANSPORT CHAIN - APPLICATION TO GLUTARIC ACIDURIA TYPE-II
被引:0
作者
:
CHRISTENSEN, E
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV COPENHAGEN,RIGSHOSP,DEPT OBSTET & GYNAECOL,DK-2100 COPENHAGEN,DENMARK
UNIV COPENHAGEN,RIGSHOSP,DEPT OBSTET & GYNAECOL,DK-2100 COPENHAGEN,DENMARK
CHRISTENSEN, E
[
1
]
机构
:
[1]
UNIV COPENHAGEN,RIGSHOSP,DEPT OBSTET & GYNAECOL,DK-2100 COPENHAGEN,DENMARK
来源
:
JOURNAL OF INHERITED METABOLIC DISEASE
|
1984年
/ 7卷
关键词
:
D O I
:
暂无
中图分类号
:
R5 [内科学];
学科分类号
:
1002 ;
100201 ;
摘要
:
引用
收藏
页码:103 / 104
页数:2
相关论文
共 9 条
[1]
IMPROVED ASSAY OF GLUTARYL-COA DEHYDROGENASE IN CULTURED-CELLS AND LIVER - APPLICATION TO GLUTARIC ACIDURIA TYPE-I
CHRISTENSEN, E
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV COPENHAGEN,RIGSHOSP,DEPT OBSTET & GYNAECOL,DK-2100 COPENHAGEN O,DENMARK
UNIV COPENHAGEN,RIGSHOSP,DEPT OBSTET & GYNAECOL,DK-2100 COPENHAGEN O,DENMARK
CHRISTENSEN, E
[J].
CLINICA CHIMICA ACTA,
1983,
129
(01)
: 91
-
97
[2]
CHRISTENSEN E, 1984, PEDIATR RES
[3]
COUDE FX, 1981, HUM GENET, V59, P263
[4]
RECURRENT HYPOGLYCEMIA ASSOCIATED WITH GLUTARIC ACIDURIA TYPE-II IN AN ADULT
DUSHEIKO, G
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
DUSHEIKO, G
KEW, MC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
KEW, MC
JOFFE, BI
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
JOFFE, BI
LEWIN, JR
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
LEWIN, JR
MANTAGOS, S
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
MANTAGOS, S
TANAKA, K
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
TANAKA, K
[J].
NEW ENGLAND JOURNAL OF MEDICINE,
1979,
301
(26)
: 1405
-
1409
[5]
GLUTARIC ACIDEMIA TYPE-II - CLINICAL, BIOCHEMICAL, AND MORPHOLOGIC CONSIDERATIONS
GOODMAN, SI
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV COLORADO, HLTH SCI CTR, SCH MED, DEPT NEUROL, DENVER, CO 80262 USA
GOODMAN, SI
STENE, DO
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV COLORADO, HLTH SCI CTR, SCH MED, DEPT NEUROL, DENVER, CO 80262 USA
STENE, DO
MCCABE, ERB
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV COLORADO, HLTH SCI CTR, SCH MED, DEPT NEUROL, DENVER, CO 80262 USA
MCCABE, ERB
NORENBERG, MD
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0
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0
h-index:
0
机构:
UNIV COLORADO, HLTH SCI CTR, SCH MED, DEPT NEUROL, DENVER, CO 80262 USA
NORENBERG, MD
SHIKES, RH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV COLORADO, HLTH SCI CTR, SCH MED, DEPT NEUROL, DENVER, CO 80262 USA
SHIKES, RH
STUMPF, DA
论文数:
0
引用数:
0
h-index:
0
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UNIV COLORADO, HLTH SCI CTR, SCH MED, DEPT NEUROL, DENVER, CO 80262 USA
STUMPF, DA
BLACKBURN, GK
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0
h-index:
0
机构:
UNIV COLORADO, HLTH SCI CTR, SCH MED, DEPT NEUROL, DENVER, CO 80262 USA
BLACKBURN, GK
[J].
JOURNAL OF PEDIATRICS,
1982,
100
(06)
: 946
-
950
[6]
C-6-C-10-DICARBOXYLIC ACIDURIA - INVESTIGATIONS OF A PATIENT WITH RIBOFLAVIN RESPONSIVE MULTIPLE ACYL-COA DEHYDROGENATION DEFECTS
GREGERSEN, N
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,INST HUMAN GENET,DK-8000 AARHUS C,DENMARK
GREGERSEN, N
WINTZENSEN, H
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KOLVRAA, S
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AARHUS UNIV,INST HUMAN GENET,DK-8000 AARHUS C,DENMARK
KOLVRAA, S
CHRISTENSEN, E
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,INST HUMAN GENET,DK-8000 AARHUS C,DENMARK
CHRISTENSEN, E
CHRISTENSEN, MF
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,INST HUMAN GENET,DK-8000 AARHUS C,DENMARK
CHRISTENSEN, MF
BRANDT, NJ
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,INST HUMAN GENET,DK-8000 AARHUS C,DENMARK
BRANDT, NJ
RASMUSSEN, K
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,INST HUMAN GENET,DK-8000 AARHUS C,DENMARK
RASMUSSEN, K
[J].
PEDIATRIC RESEARCH,
1982,
16
(10)
: 861
-
868
[7]
Gregersen N, 1980, J Inherit Metab Dis, V3, P67, DOI 10.1007/BF02312527
[8]
GLUTARIC ACIDURIA TYPE 2 - REPORT ON A PREVIOUSLY UNDESCRIBED METABOLIC DISORDER
PRZYREMBEL, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV DUSSELDORF, CHILDRENS HOSP, 4 DUSSELDORF, GERMANY
PRZYREMBEL, H
WENDEL, U
论文数:
0
引用数:
0
h-index:
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机构:
UNIV DUSSELDORF, CHILDRENS HOSP, 4 DUSSELDORF, GERMANY
WENDEL, U
BECKER, K
论文数:
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0
h-index:
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UNIV DUSSELDORF, CHILDRENS HOSP, 4 DUSSELDORF, GERMANY
BECKER, K
BREMER, HJ
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0
h-index:
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UNIV DUSSELDORF, CHILDRENS HOSP, 4 DUSSELDORF, GERMANY
BREMER, HJ
BRUINVIS, L
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV DUSSELDORF, CHILDRENS HOSP, 4 DUSSELDORF, GERMANY
BRUINVIS, L
KETTING, D
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV DUSSELDORF, CHILDRENS HOSP, 4 DUSSELDORF, GERMANY
KETTING, D
WADMAN, SK
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV DUSSELDORF, CHILDRENS HOSP, 4 DUSSELDORF, GERMANY
WADMAN, SK
[J].
CLINICA CHIMICA ACTA,
1976,
66
(02)
: 227
-
239
[9]
GLUTARIC ACIDURIA TYPE-II
SWEETMAN, L
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO, DEPT NEUROSCI, LA JOLLA, CA 92093 USA
SWEETMAN, L
NYHAN, WL
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO, DEPT NEUROSCI, LA JOLLA, CA 92093 USA
NYHAN, WL
TRAUNER, DA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO, DEPT NEUROSCI, LA JOLLA, CA 92093 USA
TRAUNER, DA
MERRITT, TA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO, DEPT NEUROSCI, LA JOLLA, CA 92093 USA
MERRITT, TA
SINGH, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO, DEPT NEUROSCI, LA JOLLA, CA 92093 USA
SINGH, M
[J].
JOURNAL OF PEDIATRICS,
1980,
96
(06)
: 1020
-
1026
←
1
→
共 9 条
[1]
IMPROVED ASSAY OF GLUTARYL-COA DEHYDROGENASE IN CULTURED-CELLS AND LIVER - APPLICATION TO GLUTARIC ACIDURIA TYPE-I
CHRISTENSEN, E
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV COPENHAGEN,RIGSHOSP,DEPT OBSTET & GYNAECOL,DK-2100 COPENHAGEN O,DENMARK
UNIV COPENHAGEN,RIGSHOSP,DEPT OBSTET & GYNAECOL,DK-2100 COPENHAGEN O,DENMARK
CHRISTENSEN, E
[J].
CLINICA CHIMICA ACTA,
1983,
129
(01)
: 91
-
97
[2]
CHRISTENSEN E, 1984, PEDIATR RES
[3]
COUDE FX, 1981, HUM GENET, V59, P263
[4]
RECURRENT HYPOGLYCEMIA ASSOCIATED WITH GLUTARIC ACIDURIA TYPE-II IN AN ADULT
DUSHEIKO, G
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
DUSHEIKO, G
KEW, MC
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
KEW, MC
JOFFE, BI
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
JOFFE, BI
LEWIN, JR
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
LEWIN, JR
MANTAGOS, S
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
MANTAGOS, S
TANAKA, K
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV WITWATERSRAND, SCH MED, DEPT MED, JOHANNESBURG 2001, SOUTH AFRICA
TANAKA, K
[J].
NEW ENGLAND JOURNAL OF MEDICINE,
1979,
301
(26)
: 1405
-
1409
[5]
GLUTARIC ACIDEMIA TYPE-II - CLINICAL, BIOCHEMICAL, AND MORPHOLOGIC CONSIDERATIONS
GOODMAN, SI
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV COLORADO, HLTH SCI CTR, SCH MED, DEPT NEUROL, DENVER, CO 80262 USA
GOODMAN, SI
STENE, DO
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV COLORADO, HLTH SCI CTR, SCH MED, DEPT NEUROL, DENVER, CO 80262 USA
STENE, DO
MCCABE, ERB
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV COLORADO, HLTH SCI CTR, SCH MED, DEPT NEUROL, DENVER, CO 80262 USA
MCCABE, ERB
NORENBERG, MD
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV COLORADO, HLTH SCI CTR, SCH MED, DEPT NEUROL, DENVER, CO 80262 USA
NORENBERG, MD
SHIKES, RH
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV COLORADO, HLTH SCI CTR, SCH MED, DEPT NEUROL, DENVER, CO 80262 USA
SHIKES, RH
STUMPF, DA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV COLORADO, HLTH SCI CTR, SCH MED, DEPT NEUROL, DENVER, CO 80262 USA
STUMPF, DA
BLACKBURN, GK
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV COLORADO, HLTH SCI CTR, SCH MED, DEPT NEUROL, DENVER, CO 80262 USA
BLACKBURN, GK
[J].
JOURNAL OF PEDIATRICS,
1982,
100
(06)
: 946
-
950
[6]
C-6-C-10-DICARBOXYLIC ACIDURIA - INVESTIGATIONS OF A PATIENT WITH RIBOFLAVIN RESPONSIVE MULTIPLE ACYL-COA DEHYDROGENATION DEFECTS
GREGERSEN, N
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,INST HUMAN GENET,DK-8000 AARHUS C,DENMARK
GREGERSEN, N
WINTZENSEN, H
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,INST HUMAN GENET,DK-8000 AARHUS C,DENMARK
WINTZENSEN, H
KOLVRAA, S
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,INST HUMAN GENET,DK-8000 AARHUS C,DENMARK
KOLVRAA, S
CHRISTENSEN, E
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,INST HUMAN GENET,DK-8000 AARHUS C,DENMARK
CHRISTENSEN, E
CHRISTENSEN, MF
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,INST HUMAN GENET,DK-8000 AARHUS C,DENMARK
CHRISTENSEN, MF
BRANDT, NJ
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,INST HUMAN GENET,DK-8000 AARHUS C,DENMARK
BRANDT, NJ
RASMUSSEN, K
论文数:
0
引用数:
0
h-index:
0
机构:
AARHUS UNIV,INST HUMAN GENET,DK-8000 AARHUS C,DENMARK
RASMUSSEN, K
[J].
PEDIATRIC RESEARCH,
1982,
16
(10)
: 861
-
868
[7]
Gregersen N, 1980, J Inherit Metab Dis, V3, P67, DOI 10.1007/BF02312527
[8]
GLUTARIC ACIDURIA TYPE 2 - REPORT ON A PREVIOUSLY UNDESCRIBED METABOLIC DISORDER
PRZYREMBEL, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV DUSSELDORF, CHILDRENS HOSP, 4 DUSSELDORF, GERMANY
PRZYREMBEL, H
WENDEL, U
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV DUSSELDORF, CHILDRENS HOSP, 4 DUSSELDORF, GERMANY
WENDEL, U
BECKER, K
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV DUSSELDORF, CHILDRENS HOSP, 4 DUSSELDORF, GERMANY
BECKER, K
BREMER, HJ
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV DUSSELDORF, CHILDRENS HOSP, 4 DUSSELDORF, GERMANY
BREMER, HJ
BRUINVIS, L
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV DUSSELDORF, CHILDRENS HOSP, 4 DUSSELDORF, GERMANY
BRUINVIS, L
KETTING, D
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV DUSSELDORF, CHILDRENS HOSP, 4 DUSSELDORF, GERMANY
KETTING, D
WADMAN, SK
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV DUSSELDORF, CHILDRENS HOSP, 4 DUSSELDORF, GERMANY
WADMAN, SK
[J].
CLINICA CHIMICA ACTA,
1976,
66
(02)
: 227
-
239
[9]
GLUTARIC ACIDURIA TYPE-II
SWEETMAN, L
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO, DEPT NEUROSCI, LA JOLLA, CA 92093 USA
SWEETMAN, L
NYHAN, WL
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO, DEPT NEUROSCI, LA JOLLA, CA 92093 USA
NYHAN, WL
TRAUNER, DA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO, DEPT NEUROSCI, LA JOLLA, CA 92093 USA
TRAUNER, DA
MERRITT, TA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO, DEPT NEUROSCI, LA JOLLA, CA 92093 USA
MERRITT, TA
SINGH, M
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO, DEPT NEUROSCI, LA JOLLA, CA 92093 USA
SINGH, M
[J].
JOURNAL OF PEDIATRICS,
1980,
96
(06)
: 1020
-
1026
←
1
→