MENTAL-RETARDATION, HYPOTONIA, AND GENERALIZED SEIZURES ASSOCIATED WITH ASTROCYTIC RESIDUAL BODIES - ULTRASTRUCTURAL STUDY

被引:7
作者
TOWFIGHI, J
GROVER, W
GONATAS, NK
机构
[1] UNIV PENN,MED SCH,447 JOHNSON PAVILION G2,PHILADELPHIA,PA 19174
[2] UNIV PENN HOSP,NEUROPATHOL LAB,PHILADELPHIA,PA
[3] ST CHRISTOPHERS HOSP,PHILADELPHIA,PA
[4] TEMPLE UNIV,MED SCH,PHILADELPHIA,PA
关键词
D O I
10.1016/S0046-8177(75)80076-1
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
引用
收藏
页码:667 / 680
页数:14
相关论文
共 57 条
[21]   ACCUMULATION OF SMOOTH CISTERNS, MULTIVESICULAR BODIES AND ZEBRA BODIES IN NEURONS - CASE OF PECULIAR STORAGE CONDITION [J].
GAMBETTI, P ;
LEVINE, RJC ;
GROVER, W ;
SUZUKI, K .
ACTA NEUROPATHOLOGICA, 1971, 18 (02) :132-+
[22]  
GONATAS N K, 1968, Pathologia Europaea, V3, P323
[23]   A CASE OF JUVENILE LIPIDOSIS - SIGNIFICANCE OF ELECTRON MICROSCOPIC AND BIOCHEMICAL OBSERVATIONS OF CEREBRAL BIOPSY [J].
GONATAS, NK ;
GOMEZ, CJ ;
STEIN, A ;
KOREY, SR ;
TERRY, RD ;
WINKLER, R .
JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY, 1963, 22 (04) :557-&
[24]   CYTOPLASMIC INCLUSIONS IN JUVENILE AMAUROTIC IDIOCY [J].
GONATAS, NK ;
GAMBETTI, P ;
TUCKER, SH ;
EVANGELISTA, I ;
BAIRD, HW .
JOURNAL OF PEDIATRICS, 1969, 75 (05) :796-+
[25]   A SECOND TYPE OF LATE INFANTILE AMAUROTIC IDIOCY WITH MULTILAMELLAR CYTOSOMES [J].
GONATAS, NK ;
GAMBETTI, P ;
BAIRD, H .
JOURNAL OF NEUROPATHOLOGY AND EXPERIMENTAL NEUROLOGY, 1968, 27 (03) :371-+
[26]   LATE INFANTILE AMAUROTIC IDIOCY (LIAI) - ANATOMOCHEMICAL REPORT OF CASE [J].
HABERLAND, C ;
WITTING, LA ;
BRUNNGRABER, EG ;
HOF, H .
NEUROLOGY, 1972, 22 (03) :305-+
[27]   LATE INFANTILE PROGRESSIVE ENCEPHALOPATHY WITH DISTURBED POLYUNSATURATED FAT METABOLISM [J].
HAGBERG, B ;
SOURANDER, P ;
SVENNERHOLM, L .
ACTA PAEDIATRICA SCANDINAVICA, 1968, 57 (06) :495-+
[28]   INFANTILE TYPE OF SO-CALLED NEURONAL CEROID-LIPOFUSCINOSIS - HISTOLOGICAL AND ELECTRON-MICROSCOPIC STUDIES [J].
HALTIA, M ;
RAPOLA, J ;
SANTAVUORI, P .
ACTA NEUROPATHOLOGICA, 1973, 26 (02) :157-170
[29]   INFANTILE TYPE OF SO-CALLED NEURONAL CEROID-LIPOFUSCINOSIS .2. MORPHOLOGICAL AND BIOCHEMICAL STUDIES [J].
HALTIA, M ;
RAPOLA, J ;
SANTAVUORI, P ;
KERANEN, A .
JOURNAL OF THE NEUROLOGICAL SCIENCES, 1973, 18 (03) :269-285
[30]   ADDITIONAL ELECTRON MICROSCOPIC OBSERVATIONS ON 2 CASES OF BATTEN-SPIELMEYER-VOGT DISEASE (NEURONAL CEROID-LIPOFUSCINOSIS) [J].
HERMAN, MM ;
RUBINSTEIN, LJ ;
MCKHANN, GM .
ACTA NEUROPATHOLOGICA, 1971, 17 (02) :85-+