Successful treatment for thrombotic thrombocytopenic purpura complicated with myeloperoxidase anti-neutrophil cytoplasmic autoantibody-associated vasculitis

被引:10
作者
Yamauchi, Yoko [1 ,2 ]
Nagatoya, Katsuyuki [2 ]
Okuno, Ayako [1 ]
Fujii, Naohiko [1 ]
Inoue, Toru [2 ]
机构
[1] Hyogo Prefectural Nishinomiya Hosp, Dept Nephrol, Nishinomiya, Hyogo, Japan
[2] Osaka Med Coll, Dept Nephrol, Osaka, Japan
来源
CLINICAL KIDNEY JOURNAL | 2010年 / 3卷 / 03期
关键词
myeloperoxidase anti-neutrophil cytoplasmic autoantibody (MPO-ANCA)-associated vasculitis; plasma exchange (PE); thrombotic thrombocytopenic purpura (TTP);
D O I
10.1093/ndtplus/sfq013
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 ; 100201 ;
摘要
Thrombotic thrombocytopenic purpura (TTP) complicated withmyeloperoxidase anti-neutrophil cytoplasmic autoantibody (MPO-ANCA)-associated vasculitis is rare and generally has a serious prognosis. We report a case wherein TTP was successfully treated with repeated plasma exchange (PE) and MPO-ANCA-associated vasculitis with corticosteroids. The renal function consequently improved such that haemodialysis could be discontinued and the patient was discharged without any significant complications.
引用
收藏
页码:279 / 281
页数:3
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