Klippel-Trenaunay Syndrome Causing Life-Threatening GI Bleeding: A Case Report and Review of the Literature

被引：15
作者：
Samo, Salih [1 ]
Sherid, Muhammed [2 ]
Husein, Husein [3 ]
Sulaiman, Samian [1 ]
Yungbluth, Margaret [4 ]
Vainder, John A. [1 ]
机构：
[1] Univ Illinois, St Francis Hosp Evanston Program, Dept Med Interne, Div Gastroenterol, 355 Ridge Ave, Chicago, IL 60202 USA
[2] CGH Med Ctr, Dept Med Interne, Div Gastroenterol, Sterling, IL 61081 USA
[3] Univ Tishreen, Dept Med Interne, Div Gastroenterol, Latakia, Syria
[4] Univ Illinois, St Francis Hosp Evanston Program, Dept Pathol, Chicago, IL 60202 USA
来源：
CASE REPORTS IN GASTROINTESTINAL MEDICINE | 2013年 / 2013卷
关键词：
D O I：
10.1155/2013/813653
中图分类号：
R57 [消化系及腹部疾病];
学科分类号：
摘要：
Klippel-Trenaunay syndrome (KTS) is a rare congenital syndrome of vascularmalformations and soft tissue and bone hypertrophy. Vascular malformations can affect multiple organ systems. Involvement of the gastrointestinal (GI) tract is uncommon in KTS, but it can be a source of life-threatening bleeding. We report a case of a 32-year-oldmale with a known diagnosis ofKTS who presented with a life-threatening rectal bleeding and was treated with proctosigmoidectomy and massive blood products transfusion. He expired after a long hospitalization. We then review the literature on KTS and management of some of its complications.
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