PYRUVATE-CARBOXYLASE IN HUMAN LIVER - APPARENT LOSS OF A COMPONENT OF CATALYTIC ACTIVITY IN A FORM OF LACTIC ACIDOSIS WITH HYPOGLYCEMIA

被引:7
作者
DELVIN, E [1 ]
SCRIVER, CR [1 ]
NEAL, JL [1 ]
机构
[1] CHILDRENS HOSP,DEBELLE LAB BIOCHEM GENET,2300 TUPPER ST,MONTREAL 108,QUEBEC,CANADA
来源
BIOCHEMICAL MEDICINE | 1974年 / 10卷 / 02期
关键词
D O I
10.1016/0006-2944(74)90012-X
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:97 / 106
页数:10
相关论文
共 21 条
[1]   IMMUNOCHEMICAL STUDIES WITH SOLUBLE AND MITOCHRONDRIAL PYRUVATE CARBOXYLASE ACTIVITIES FROM RAT TISSUES [J].
BALLARD, FJ ;
HANSON, RW ;
RESHEF, L .
BIOCHEMICAL JOURNAL, 1970, 119 (04) :735-&
[2]  
BARDEN RE, 1972, J BIOL CHEM, V247, P1323
[3]   SUCCINIC DEHYDROGENASE [J].
BONNER, WD .
METHODS IN ENZYMOLOGY, 1955, 1 :722-729
[4]   STUDIES ON PYRUVATE CARBOXYLASE IN RAT AND HUMAN LIVER [J].
BRECH, W ;
SHRAGO, E ;
WILKEN, D .
BIOCHIMICA ET BIOPHYSICA ACTA, 1970, 201 (02) :145-&
[5]  
BRUNETTE MG, 1972, PEDIATRICS, V50, P702
[6]  
De Duve C., 1955, BIOCHEM J, V60, P605
[7]  
EXTON JH, 1968, J BIOL CHEM, V243, P4189
[8]  
Fiske CH, 1925, J BIOL CHEM, V66, P375
[9]   TISSUE FRACTIONATION STUDIES .4. COMPARATIVE STUDY OF THE BINDING OF ACID PHOSPHATASE, BETA-GLUCURONIDASE AND CATHEPSIN BY RAT-LIVER PARTICLES [J].
GIANETTO, R ;
DUVE, CD .
BIOCHEMICAL JOURNAL, 1955, 59 (03) :433-438
[10]  
KEECH DB, 1963, J BIOL CHEM, V238, P2609