BIOSYNTHESIS OF ELECTRON-TRANSFER FLAVOPROTEIN IN A CELL-FREE SYSTEM AND IN CULTURED HUMAN-FIBROBLASTS - DEFECT IN THE ALPHA SUBUNIT SYNTHESIS IS A PRIMARY LESION IN GLUTARIC ACIDURIA TYPE-II

被引：57

作者：

IKEDA, Y ^{[1
]}

KEESE, SM ^{[1
]}

TANAKA, K ^{[1
]}

机构：

[1] YALE UNIV,SCH MED,DEPT HUMAN GENET,333 CEDAR ST,NEW HAVEN,CT 06510

来源：

JOURNAL OF CLINICAL INVESTIGATION | 1986年 / 78卷 / 04期

关键词：

D O I：

10.1172/JCI112691

中图分类号：

R-3 [医学研究方法]; R3 [基础医学];

学科分类号：

1001 ;

摘要：

引用

页码：997 / 1002

页数：6

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