Innovative technique for repair of Tetralogy of Fallot with absent pulmonary, valve syndrome using autologous pericardial patch with monocusp valve

被引：1

作者：

Reddy K.P. ^{[1
]}

Dharmapuram A.K. ^{[1
]}

Swain S.K. ^{[1
]}

Ramdoss N. ^{[1
]}

Agarwal R. ^{[1
]}

Gouthmi V. ^{[1
]}

Sundararaghavan S. ^{[1
]}

Murthy K.S. ^{[1
,2
]}

机构：

[1] Department of Pediatric Cardiac Surgery, Apollo Children's Heart Hospital, Jubilee Hills, Hyderabad

[2] Innova Children's Heart Hospital Tarnaka, Secunderabad, 017, Moula Ali Road

来源：

Indian Journal of Thoracic and Cardiovascular Surgery | 2008年 / 24卷 / 3期

关键词：

Pulmonary arteries; Sternotomy; Ventricular septal defect;

D O I：

10.1007/s12055-008-0034-0

中图分类号：

学科分类号：

摘要：

Background: Conventional surgery for absent pulmonary valve is repair with valve conduit between right ventricle (RV) and Pulmonary artery (PA). We describe a technique of repairing absent pulmonary valve with autologous pericardial patch with monocusp valve, without using valve conduit and its results. Methods: From February 2004 to September 2006, 14 consecutive patients with absent pulmonary valve syndrome (APVS) were repaired using this technique. Age range was 5-168 months (median- 24 months) and weight range was 6-31 kgs (median-10 kgs), 5 were infants. Varying degree of respiratory symptoms were present in all patients including tachypnoea, difficulty in feeding, wheezing, recurrent pneumonia and cyanosis. Repair consisted of ventricular septal defect closure, relief of right ventricular outflow obstruction with autologous pericardial patch with monocusp valve. PA aneurysmorrhaphy and PA reduction arterioplasty were done in selected cases. Result: There was one mortality. The follow up ranged from 12 months to 36 months, respiratory symptoms disappeared or were significantly improved in all patients. Two dimensional (2D) Echo showed trivial to mild pulmonary regurgitation (PR) in 11 patients & moderate in two patients. One patient had minimal right ventricular outflow tract (RVOT) obstruction. None of them required reintervention. Conclusion: New innovative technique of using autologous pericardial patch with monocusp valve in absent pulmonary valve syndrome can be safely performed in infants and children. It avoids conduit related problems like reintervention and is economical. Our early and midterm results are encouraging, however long term results are awaited. © 2008 Indian Association of Cardiovascular-Thoracic Surgeons.

引用

页码：167 / 170

页数：3

共 24 条

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