A Case of Wilson-Mikity Syndrome With High Serum KL-6 Levels

被引:5
|
作者
Takeshi Takami
Atsushi Kumada
Yukito Takei
Tasuku Miyajima
Akinori Hoshika
机构
[1] Tokyo Medical University,Department of Pediatrics
[2] 6-7-1 Nishishinjuku,undefined
[3] Shinjuku-ku,undefined
关键词
D O I
10.1038/sj.jp.7210830
中图分类号
学科分类号
摘要
KL-6 and surfactant protein D (SP-D) serum concentrations are known to rise in adult patients with various types of interstitial pneumonia. We evaluated the time course of serum KL-6, SP-D, and lactate dehydrogenase (LDH) levels in an infant with Wilson-Mikity syndrome. In this case, serum KL-6 levels correlated with clinical symptoms better than serum SP-D and LDH levels. The findings of this case suggest that high serum levels of KL-6 show activity of interstitial lung disease of Wilson-Mikity syndrome.
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页码:56 / 58
页数:2
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