A rare co-occurrence of duchenne muscular dystrophy, congenital adrenal hypoplasia and glycerol kinase deficiency due to Xp21 contiguous gene deletion syndrome: case report

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作者
Asanka Rathnasiri
Udara Senarathne
Visvalingam Arunath
Thabitha Hoole
Ishara Kumarasiri
Oshanie Muthukumarana
Eresha Jasinge
Sachith Mettananda
机构
[1] Colombo North Teaching Hospital,Department of Biochemistry, Faculty of Medical Sciences
[2] University of Sri Jayewardenepura,Department of Paediatrics, Faculty of Medicine
[3] Lady Ridgeway Children’s Hospital,undefined
[4] University of Kelaniya,undefined
来源
BMC Endocrine Disorders | / 21卷
关键词
Contiguous gene deletion syndrome; Congenital adrenal hypoplasia; Duchenne muscular dystrophy; Glycerol kinase deficiency;
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[1]  
Cole DEC(1994)Congenital adrenal hypoplasia, Duchenne muscular dystrophy, and glycerol kinase deficiency: Importance of laboratory investigations in delineating a contiguous gene deletion syndrome Clin Chem 40 2099-103
[2]  
Clarke LA(2011)A neonate with contiguous deletion syndrome in XP21 J Pediatr Endocrinol Metab 24 1095-8
[3]  
Riddell DC(1987)Familial deletion of Xp21.2 with glycerol kinase deficiency and congenital adrenal hypoplasia Hum Genet 77 379-83
[4]  
Samson KA(1986)Duchenne muscular dystrophy with adrenal insufficiency and glycerol kinase deficiency: High resolution cytogenetic analysis with molecular, biochemical, and clinical studies J Med Genet 23 501-8
[5]  
Seltzer WK(1988)Deletion proximal to DXS68 locus (L1 probe site) in a boy with Duchenne muscular dystrophy, glycerol kinase deficiency, and adrenal hypoplasia Hum Genet 78 222-7
[6]  
Salisbury S(1998)Congenital adrenal hypoplasia: Clinical spectrum, experience with hormonal diagnosis, and report on new point mutations of the DAX-1 gene J Clin Endocrinol Metab 83 2666-74
[7]  
Sevim U(1987)Congenital adrenal hypoplasia, myopathy, and glycerol kinase deficiency: Molecular genetic evidence for deletions Am J Hum Genet 40 212-27
[8]  
Fatma D(2004)Glycerol kinase deficiency: residual activity explained by reduced transcription and enzyme conformation Eur J Hum Genet 12 424-32
[9]  
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