Prednisolone-responsive primary sclerosing cholangitis with autoimmune hemolytic anemia: a case report and review of the literature

被引：0
作者：
Toshihiro Kawaguchi
Teruko Arinaga-Hino
Satoshi Morishige
Shinji Mizuochi
Mitsuhiko Abe
Kazuya Kunitake
Tomoya Sano
Keisuke Amano
Reiichiro Kuwahara
Tatsuya Ide
Koji Nagafuji
Takuji Torimura
机构：
[1] Kurume University School of Medicine,Division of Gastroenterology, Department of Medicine
[2] Kurume University School of Medicine,Division of Hematology and Oncology, Department of Medicine
[3] Kurume University School of Medicine,Department of Pathology
[4] Nishinihon Hospital,Department of Gastroenterology
来源：
Clinical Journal of Gastroenterology | 2021年 / 14卷
关键词：
Primary sclerosing cholangitis; Autoimmune hemolytic anemia; Prednisolone;
D O I：
暂无
中图分类号：
学科分类号：
摘要：
We report a case of primary sclerosing cholangitis (PSC) with autoimmune hemolytic anemia (AIHA). A 47-year-old woman was diagnosed with PSC. One year later, she was admitted to our hospital for jaundice and fatigue. Magnetic resonance cholangiopancreatography (MRCP) showed worsening of the biliary stricture, and rapidly progressive anemia developed simultaneously. Based on the various laboratory findings, she was diagnosed with AIHA. The administration of prednisolone improved not only the anemia but also the biliary stricture. This case is impactful, as there are few case reports of PSC with AIHA. In addition, we were able to observe the changes in imaging findings using MRCP over time.
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页码：330 / 335
页数：5
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