A 73-year-old Japanese woman was diagnosed with type 1 autoimmune pancreatitis (AIP) without kidney lesions. She was treated with prednisolone (PSL) 30 mg/day, and her AIP symptoms promptly improved, after which the PSL dose was gradually tapered to 5 mg/day. Her renal function had remained normal (serum creatinine 0.7 mg/dL) until 1 year before the current admission without any imaging abnormalities in the kidney. However, during this past year her renal function gradually declined (serum creatinine 1.1 mg/dL). Follow-up computed tomography incidentally revealed unilateral renal atrophy, which rapidly progressed during the subsequent 10-month period without left kidney atrophy. A diagnosis of IgG4-RKD probably due to TIN was made, and we increased the dose of prednisolone to 30 mg/day. 1 month after administration, multiple low-density lesions on both kidneys were improved slightly but almost all lesions persisted as atrophic scars. Our case suggested that unilateral renal atrophy can develop in patients with IgG4-related tubulointerstitial nephritis without hydronephrosis caused by retroperitoneal fibrosis, and that monitoring the serum creatinine levels is not always sufficient, thereby highlighting the importance of regular imaging monitoring to detect newly developing kidney lesions.
机构:
Kanazawa Univ, Grad Sch Med, Kanazawa Univ Hosp, Div Rheumatol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, JapanKanazawa Univ, Grad Sch Med, Kanazawa Univ Hosp, Div Rheumatol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, Japan
Takeji, Akari
Yamada, Kazunori
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Kanazawa Univ, Grad Sch Med, Kanazawa Univ Hosp, Div Rheumatol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, Japan
Kanazawa Univ, Grad Sch Med Sci, Dept Adv Res Community Med, Kanazawa, Ishikawa, JapanKanazawa Univ, Grad Sch Med, Kanazawa Univ Hosp, Div Rheumatol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, Japan
Yamada, Kazunori
Inoue, Dai
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Kanazawa Univ, Grad Sch Med Sci, Dept Radiol, Kanazawa, Ishikawa, JapanKanazawa Univ, Grad Sch Med, Kanazawa Univ Hosp, Div Rheumatol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, Japan
Inoue, Dai
Mizushima, Ichiro
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Kanazawa Univ, Grad Sch Med, Kanazawa Univ Hosp, Div Rheumatol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, JapanKanazawa Univ, Grad Sch Med, Kanazawa Univ Hosp, Div Rheumatol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, Japan
Mizushima, Ichiro
Hara, Satoshi
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Kanazawa Univ, Grad Sch Med, Kanazawa Univ Hosp, Div Rheumatol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, JapanKanazawa Univ, Grad Sch Med, Kanazawa Univ Hosp, Div Rheumatol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, Japan
Hara, Satoshi
Ito, Kiyoaki
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Kanazawa Univ, Grad Sch Med, Kanazawa Univ Hosp, Div Rheumatol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, JapanKanazawa Univ, Grad Sch Med, Kanazawa Univ Hosp, Div Rheumatol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, Japan
Ito, Kiyoaki
Fujii, Hiroshi
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Kanazawa Univ, Grad Sch Med, Kanazawa Univ Hosp, Div Rheumatol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, JapanKanazawa Univ, Grad Sch Med, Kanazawa Univ Hosp, Div Rheumatol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, Japan
Fujii, Hiroshi
Nakajima, Kenichi
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Kanazawa Univ Hosp, Dept Nucl Med, Kanazawa, Ishikawa, JapanKanazawa Univ, Grad Sch Med, Kanazawa Univ Hosp, Div Rheumatol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, Japan
Nakajima, Kenichi
Mizutomi, Kazuaki
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Kaga Med Ctr, Internal Med, Kaga, Ishikawa, JapanKanazawa Univ, Grad Sch Med, Kanazawa Univ Hosp, Div Rheumatol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, Japan
Mizutomi, Kazuaki
Yamagishi, Masakazu
论文数: 0引用数: 0
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机构:
Kanazawa Univ, Grad Sch Med, Div Cardiol, Kanazawa, Ishikawa, JapanKanazawa Univ, Grad Sch Med, Kanazawa Univ Hosp, Div Rheumatol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, Japan
Yamagishi, Masakazu
Kawano, Mitsuhiro
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机构:
Kanazawa Univ, Grad Sch Med, Kanazawa Univ Hosp, Div Rheumatol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, JapanKanazawa Univ, Grad Sch Med, Kanazawa Univ Hosp, Div Rheumatol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, Japan
机构:
Mayo Clin, Dept Lab Med & Pathol, Div Anat Pathol, Rochester, MN 55905 USAMayo Clin, Dept Lab Med & Pathol, Div Anat Pathol, Rochester, MN 55905 USA
Cornell, Lynn D.
CURRENT OPINION IN NEPHROLOGY AND HYPERTENSION,
2012,
21
(03):
: 279
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288
机构:
Mayo Clin, Div Anat Pathol, Dept Lab Med & Pathol, Rochester, MN 55905 USAMayo Clin, Div Anat Pathol, Dept Lab Med & Pathol, Rochester, MN 55905 USA
机构:
Sorbonne Univ, Hop Tenon, AP HP, Inserm,Dept Nephrol,UMRS 1155, F-75020 Paris, FranceSorbonne Univ, Hop Tenon, AP HP, Inserm,Dept Nephrol,UMRS 1155, F-75020 Paris, France
Boffa, Jean-Jacques
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Esteve, Emmanuel
Buob, David
论文数: 0引用数: 0
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Sorbonne Univ, Hop Tenon, AP HP, Dept Pathol,Inserm,UMRS 1155, F-75020 Paris, FranceSorbonne Univ, Hop Tenon, AP HP, Inserm,Dept Nephrol,UMRS 1155, F-75020 Paris, France
机构:
Kanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Rheumatol, Takara Machi 13-1, Kanazawa, Ishikawa 9208640, Japan
Ishikawa Prefectural Cent Hosp, Div Nephrol & Rheumatol, Dept Internal Med, Kanazawa, Ishikawa, JapanKanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Rheumatol, Takara Machi 13-1, Kanazawa, Ishikawa 9208640, Japan
Mizushima, Ichiro
Yamamoto, Motohisa
论文数: 0引用数: 0
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Sapporo Med Univ, Dept Internal Med 1, Chuo Ku, South 1,West 16, Sapporo, Hokkaido 0608543, JapanKanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Rheumatol, Takara Machi 13-1, Kanazawa, Ishikawa 9208640, Japan
Yamamoto, Motohisa
Inoue, Dai
论文数: 0引用数: 0
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机构:
Kanazawa Univ, Dept Radiol, Grad Sch Med Sci, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, JapanKanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Rheumatol, Takara Machi 13-1, Kanazawa, Ishikawa 9208640, Japan
Inoue, Dai
Nishi, Shinichi
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机构:
Kobe Univ, Grad Sch Med, Div Nephrol, Chuo Ku, 7-5-1 Kusunoki, Kobe, Hyogo 6500017, Japan
Kobe Univ, Grad Sch Med, Kidney Ctr, Chuo Ku, 7-5-1 Kusunoki, Kobe, Hyogo 6500017, JapanKanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Rheumatol, Takara Machi 13-1, Kanazawa, Ishikawa 9208640, Japan
Nishi, Shinichi
Taniguchi, Yoshinori
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机构:
Kochi Univ, Dept Endocrinol Metab & Nephrol, Kochi Med Sch, Nanko Ku, Oko Cho, Nankoku, Kochi 7838505, JapanKanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Rheumatol, Takara Machi 13-1, Kanazawa, Ishikawa 9208640, Japan
Taniguchi, Yoshinori
Ubara, Yoshifumi
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机构:
Toranomon Gen Hosp, Nephrol Ctr, Minato Ku, Toranomon 2-2-2, Tokyo 1058470, Japan
Toranomon Gen Hosp, Okinaka Mem Inst Med Res, Minato Ku, Toranomon 2-2-2, Tokyo 1058470, JapanKanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Rheumatol, Takara Machi 13-1, Kanazawa, Ishikawa 9208640, Japan
Ubara, Yoshifumi
Matsui, Shoko
论文数: 0引用数: 0
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机构:
Toyama Univ, Hlth Adm Ctr, 2630 Sugitani, Toyama, Toyama 9300194, JapanKanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Rheumatol, Takara Machi 13-1, Kanazawa, Ishikawa 9208640, Japan
Matsui, Shoko
Yasuno, Tetsuhiko
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机构:
Fukuoka Univ, Div Nephrol & Rheumatol, Dept Internal Med, Jonan Ku, 7-45-1 Nanakuma, Fukuoka 8140180, JapanKanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Rheumatol, Takara Machi 13-1, Kanazawa, Ishikawa 9208640, Japan
Yasuno, Tetsuhiko
Nakashima, Hitoshi
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机构:
Fukuoka Univ, Div Nephrol & Rheumatol, Dept Internal Med, Jonan Ku, 7-45-1 Nanakuma, Fukuoka 8140180, JapanKanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Rheumatol, Takara Machi 13-1, Kanazawa, Ishikawa 9208640, Japan
Nakashima, Hitoshi
Takahashi, Hiroki
论文数: 0引用数: 0
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机构:
Sapporo Med Univ, Dept Internal Med 1, Chuo Ku, South 1,West 16, Sapporo, Hokkaido 0608543, JapanKanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Rheumatol, Takara Machi 13-1, Kanazawa, Ishikawa 9208640, Japan
Takahashi, Hiroki
Yamada, Kazunori
论文数: 0引用数: 0
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机构:
Kanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Rheumatol, Takara Machi 13-1, Kanazawa, Ishikawa 9208640, JapanKanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Rheumatol, Takara Machi 13-1, Kanazawa, Ishikawa 9208640, Japan
Yamada, Kazunori
Nomura, Hideki
论文数: 0引用数: 0
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机构:
Kanazawa Univ Hosp, Dept Gen Med, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, JapanKanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Rheumatol, Takara Machi 13-1, Kanazawa, Ishikawa 9208640, Japan
Nomura, Hideki
Yamagishi, Masakazu
论文数: 0引用数: 0
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机构:
Kanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Cardiol, 13-1 Takara Machi, Kanazawa, Ishikawa 9208640, JapanKanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Rheumatol, Takara Machi 13-1, Kanazawa, Ishikawa 9208640, Japan
Yamagishi, Masakazu
Saito, Takao
论文数: 0引用数: 0
h-index: 0
机构:
Fukuoka Univ, Div Nephrol & Rheumatol, Dept Internal Med, Jonan Ku, 7-45-1 Nanakuma, Fukuoka 8140180, JapanKanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Rheumatol, Takara Machi 13-1, Kanazawa, Ishikawa 9208640, Japan
Saito, Takao
Kawano, Mitsuhiro
论文数: 0引用数: 0
h-index: 0
机构:
Kanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Rheumatol, Takara Machi 13-1, Kanazawa, Ishikawa 9208640, JapanKanazawa Univ, Dept Cardiovasc & Internal Med, Grad Sch Med, Div Rheumatol, Takara Machi 13-1, Kanazawa, Ishikawa 9208640, Japan