Hemophagocytic syndrome in adult-onset Still’s disease (AOSD): A must for biologics?—Case report and brief review of the literature

被引：0
作者：
Urs Bürgi
Adriana Mendez
Paul Hasler
Hans Dieter Hüllstrung
机构：
[1] Kantonsspital Aarau,Department of Medicine
[2] Kantonsspital Aarau,Department of Laboratory Medicine
[3] Kantonsspital Aarau,Department of Rheumatology
[4] Bethesda-Spital Basel,Department of Rheumatology
来源：
Rheumatology International | 2012年 / 32卷
关键词：
Adult-onset Still’s disease; Biological products; Hemophagocytic lymphohistiocytosis; Reactive hemophagocytic syndrome;
D O I：
暂无
中图分类号：
学科分类号：
摘要：
A case of adult-onset Still’s disease complicated by hemophagocytic lymphohistiocytosis is reported. Its management is being discussed on the background of the latest literature with special regard on the use of high-dose corticosteroids and immunosuppressive agents.
引用
收藏
页码：3269 / 3272
页数：3
相关论文
共 25 条
[1]  
Still GF(1897)On a form of chronic joint disease in children Med Chir Trans 80 47-1691
[2]  
Baywaters EG(1971)Stills disease in the adults Ann Rheum Dis 30 121-131
[3]  
Yamaguchi M(1992)Preliminary criteria for classification of adult Still’s disease J Rheumatol 19 424-182
[4]  
Ohta A(2006)Reactive haemophagocytic syndrome in adult-onset Still’s disease: a report of six patients and a review of the literature Ann Rheum Dis 65 1596-1803
[5]  
Tsunematsu T(2008)Clinical features of haemophagocytic syndrome in patients with systemic autoimmune diseases: analysis of 30 cases Rheumatology 47 1686-308
[6]  
Arlet JB(2007)HLH-2004: diagnostic and therapeutic guidelines for hemophagocytic lymphohistiocytosis Pediatr Blood Cancer 48 124-undefined
[7]  
Le TH(2006)Characteristics and long-term outcome of 15 episodes of systemic Lupus erythematodes-associated hemophagocytic syndrome Medicine 85 169-undefined
[8]  
Marinho A(2005)Rapid response to Anakinra in patients with refractory adult-onset Still’s disease Arthritis Rheum 52 1794-undefined
[9]  
Fukaya S(2008)Interleukin-1 receptor antagonist (anakinra) treatment in patients with systemic-onset juvenile idiopathic arthritis or adult onset Still disease: preliminary experience in France Ann Rheum Dis 67 302-undefined
[10]  
Yasuda S(undefined)undefined undefined undefined undefined-undefined
123