Chronicle of a death foretold: a case of catastrophic vascular Behcet’s disease

被引：0
作者：
David Planer
David Leibowitz
Yair Elitzur
Amit Korach
Nurith Hiller
Tova Chajek-Shaul
机构：
[1] Hadassah-Hebrew University Medical Center,Internal Medicine
[2] Mount Scopus Campus,Cardiology Department
[3] Hadassah-Hebrew University Medical Center,Cardiothoracic Surgery
[4] Hadassah-Hebrew University Medical Center,Radiology Department
[5] Hadassah-Hebrew University Medical Center,undefined
来源：
Clinical Rheumatology | 2007年 / 26卷
关键词：
Aortic aneurysm; Behcet’s disease; Computed tomography; Echocardiography; Immunosuppression;
D O I：
暂无
中图分类号：
学科分类号：
摘要：
A 20-year-old man with Behcet's disease characterized by recurrent arterial aneurysms presented with a new aortic root aneurysm. This patient previously had aneurysms of the coronary arteries and vein, as well as ruptured renal artery aneurysm. Chronic maintenance immunosuppressive therapy was recommended due to the catastrophic nature of the disease, which the patient refused to take. The patient died shortly after admission. This case demonstrates the unique catastrophic natural history of vascular Behcet's disease with recurrent life-threatening arterial events, and this case stresses the therapeutic dilemma of maintenance immunosuppressive therapy in selected patients.
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页码：457 / 459
页数：2
相关论文
共 72 条
[1]  
Behcet H(1937)Uber rezidivierende, aphtose durch ein virus verursachte Geschwure am Mund, am Auge und an den Genitalien Dermatol Wochenschr 105 1152-1157
[2]  
Chajek T(1975)Behcet’s disease. Report of 41 cases and a review of the literature Medicine (Baltimore) 54 179-196
[3]  
Fainaru M(2003)The long-term mortality and morbidity of Behcet syndrome: a 2-decade outcome survey of 387 patients followed at a dedicated center Medicine (Baltimore) 82 60-76
[4]  
Kural-Seyahi E(1992)Vascular involvement in Behcet’s disease J Rheumatol 19 402-410
[5]  
Fresko I(1989)Pulmonary manifestations in Behcet’s syndrome Chest 95 585-589
[6]  
Seyahi N(2000)Neutrophil and endothelial cell activation in the vasa vasorum in vasculo-Behcet disease Histopathology 36 362-371
[7]  
Ozyazgan Y(1997)A fatal case of Behcet’s disease associated with multiple cardiovascular lesions Int J Cardiol 59 267-273
[8]  
Mat C(1992)The repetitive vascular catastrophes of Behcet’s disease: a case report with review of the literature Ann Vasc Surg 6 85-89
[9]  
Hamuryudan V(2003)Endovascular therapy combined with immunosuppressive treatment for pseudoaneurysms in patients with Behcet’s disease J Endovasc Ther 10 75-80
[10]  
Yurdakul S(2001)Azathiopine-steroid combination therapy for pulmonary arterial aneurysms in Behcet’s disease Rheumatol Int 20 171-174
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