Primary primitive neuroectodermal tumor (PNET) of the kidney with venous thrombus

被引:13
作者
B. Sivaramakrishna
Om Prakash Mundada
Monish Aron
Manju Aron
M. Vijayaraghavan
机构
[1] Department of Urology, All India Inst. of Medical Sciences
[2] Department of Pathology, All India Inst. of Medical Sciences
关键词
Kidney; Neuroectodermal; PNET; Primitive; Tumor; Venous thrombus;
D O I
10.1023/B:UROL.0000022921.65697.96
中图分类号
学科分类号
摘要
Primitive neuroectodermal tumors of the kidney are rare, the diagnosis usually being made at histopathology. A young adult presented with a painful left renal mass. CT Scan of the abdomen revealed a large necrotic tumor of the left kidney. At surgery the patient was found to have a venous thrombus confined to the renal vein. Radical nephrectomy was done. Histopathology showed a round cell neoplasm with typical Homer Wright rosette formation and positive staining for neuron specific enolase (NSE) and MIC-2 on immunohistochemistry. The patient is undergoing multidrug chemotherapy and is alive and well at a follow up of nine months. © 2004 Kluwer Academic Publishers.
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收藏
页码:311 / 312
页数:1
相关论文
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