Congenital long QT syndrome

被引：0
作者：
Lia Crotti
Giuseppe Celano
Federica Dagradi
Peter J Schwartz
机构：
[1] Blood and Heart,Section of Cardiology, Department of Lung
[2] University of Pavia,Department of Cardiology
[3] IRCCS Fondazione Policlinico S. Matteo,Molecular Cardiology Laboratory
[4] IRCCS Fondazione Policlinico S. Matteo,Laboratory of Cardiovascular Genetics
[5] IRCCS Istituto Auxologico,Department of Medicine
[6] University of Stellenbosch,Cardiovascular Genetics Laboratory, Hatter Institute for Cardiovascular Research, Department of Medicine
[7] University of Cape Town,undefined
来源：
Orphanet Journal of Rare Diseases | / 3卷
关键词：
Sudden Infant Death Syndrome; Implantable Cardioverter Defibrillator; Mexiletine; Syncopic Episode; Catecholaminergic Polymorphic Ventricular Tachycardia;
D O I：
暂无
中图分类号：
学科分类号：
摘要：
Congenital long QT syndrome (LQTS) is a hereditary cardiac disease characterized by a prolongation of the QT interval at basal ECG and by a high risk of life-threatening arrhythmias. Disease prevalence is estimated at close to 1 in 2,500 live births.
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