Extra Mammary Paget’s Disease of Vulva—a Case Report

被引：2

作者：

Tomar T.S. ^{[1
]}

Sambasivan S. ^{[1
]}

Nair R.P. ^{[1
]}

Thomas S. ^{[1
]}

Ramadas P.T. ^{[1
]}

机构：

[1] Regional Cancer Centre (RCC), Medical College Campus, Trivandrum, 695011, Kerala

来源：

Indian Journal of Surgical Oncology | 2016年 / 7卷 / 4期

关键词：

Extra mammary Paget’s disease; Vulva; Vulvar disease;

D O I：

10.1007/s13193-016-0551-z

中图分类号：

学科分类号：

摘要：

Extra mammary Paget’s disease (EMPD) is a rare condition involving the vulva, anogenital region, and axilla. Vulvar disease usually presents as a slow growing well-defined itchy plaque with crustations or ulcerations over the affected area in postmenopausal women. Well-established guidelines for diagnosis and management are not available for this rare condition. Our patient is a 64-year-old postmenopausal woman with a history of similar complaints of 2 years duration, not responding to multiple topical treatments. She was diagnosed with EMPD on incisional biopsy and treated with surgery at our centre. © 2016, Indian Association of Surgical Oncology.

引用

页码：488 / 490

页数：2

共 11 条

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