Bile duct carcinoma associated with congenital biliary dilatation in a 16-year-old female: a case report and literature review

被引：0
作者：
Hideki Izumi
Naoki Yazawa
Daisuke Furukawa
Yoshihito Masuoka
Misuzu Yamada
Taro Mashiko
Yohei Kawashima
Masami Ogawa
Yoshiaki Kawaguchi
Tetsuya Mine
Kenichi Hirabayashi
Toshio Nakagohri
机构：
[1] Tokai University School of Medicine,Department of Gastrointestinal Surgery
[2] Tokai University School of Medicine,Department of Internal Medicine
[3] Tokai University School of Medicine,Department of Pathology
来源：
Surgical Case Reports | / 2卷 / 1期
关键词：
Congenital biliary dilatation; Pancreaticobiliary maljunction; Bile duct carcinoma; Pancreaticoduodenectomy;
D O I：
10.1186/s40792-016-0132-y
中图分类号：
学科分类号：
摘要：
We encountered a very rare case of bile duct carcinoma associated with congenital biliary dilatation (CBD) in a 16-year-old female who was admitted to our hospital because of right upper abdominal pain and vomiting. Abdominal computed tomography demonstrated a cystic dilatation of the common bile duct measuring 7 cm in diameter and two enhanced tumors 4 cm in diameter located in the inferior bile duct and middle bile duct. Magnetic resonance cholangiopancreatography clearly demonstrated a cystic dilatation of the extrahepatic bile duct (Todani’s CBD classification: type 4-A). Endoscopic retrograde cholangiopancreatography also revealed two tumors. Biopsy results of one of the tumors confirmed adenocarcinoma. Excision of the perihilar bile duct and subtotal stomach-preserving pancreaticoduodenectomy with dissection of the major lymph nodes were performed. A postoperative histopathologic examination revealed a well-differentiated tubular adenocarcinoma, which remained within the mucosal layer, and no lymph node metastasis was found. The postoperative course was uneventful, and the patient was discharged 10 days after surgery and has remained disease-free for 21 months.
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