Beneath the floor: re-analysis of neurodevelopmental outcomes in untreated Hurler syndrome

被引:0
作者
Elsa G. Shapiro
Chester B. Whitley
Julie B. Eisengart
机构
[1] University of Minnesota,Department of Pediatrics
[2] Shapiro Neuropsychology Consulting,Department of Experimental and Clinical Pharmacology
[3] LLC,undefined
[4] University of Minnesota,undefined
来源
Orphanet Journal of Rare Diseases | / 13卷
关键词
Mucopolysaccharidosis type I; Developmental quotient; Neurodegenerative disease; Age equivalent; Cognitive decline; Newborn screening; Natural history;
D O I
暂无
中图分类号
学科分类号
摘要
引用
收藏
相关论文
共 135 条
[1]  
Shapiro EG(2015)Neurocognition across the spectrum of mucopolysaccharidosis type I: age, severity, and treatment Mol Genet Metab 116 61-68
[2]  
Nestrasil I(2015)Long-term outcome of Hurler syndrome patients after hematopoietic cell transplantation: an international multicenter study Blood 125 2164-2172
[3]  
Rudser K(2014)Early treatment is associated with improved cognition in Hurler syndrome Ann Neurol 76 747-753
[4]  
Delaney K(2017)Mucopolysaccharidosis type I newborn screening: best practices for diagnosis and management J Pediatr 182 363-370
[5]  
Kovac V(2017)Early disease progression of hurler syndrome Orphanet J Rare Dis 12 32-176
[6]  
Ahmed A(1999)Bone marrow transplantation as effective treatment of central nervous system disease in globoid cell leukodystrophy, metachromatic leukodystrophy, adrenoleukodystrophy, mannosidosis, fucosidosis, aspartylglucosaminuria, Hurler, Maroteaux-Lamy, and Sly syndromes, and Gaucher disease type III Curr Opin Neurol 12 167-287
[7]  
Yund B(1996)Outcome of unrelated donor bone marrow transplantation in 40 children with hurler syndrome Blood 87 4894-69
[8]  
Orchard PJ(1998)Hurler syndrome: II. Outcome of HLA-genotypically identical sibling and HLA-haploidentical related donor bone marrow transplantation in fifty-four children Blood 91 2601-75
[9]  
Eisengart J(2016)A prospective natural history study of mucopolysaccharidosis type IIIA J Pediatr 170 278-29
[10]  
Niklason GR(2016)Neurocognitive clinical outcome assessments for inborn errors of metabolism and other rare conditions Mol Genet Metab 118 65-190