Quantitative connection between polyglutamine aggregation kinetics and neurodegenerative process in patients with Huntington’s disease

被引:0
作者
Keizo Sugaya
Shiro Matsubara
机构
[1] Tokyo Metropolitan Neurological Hospital,Department of Neurology
来源
Molecular Neurodegeneration | / 7卷
关键词
Huntington’s disease; Polyglutamine aggregation; SCA3; Stochastic kinetics model; Cumulative damage; One-hit model; Nucleated growth polymerization; Nucleation; Elongation;
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