Does the effect of comprehensive respiratory physiotherapy home-program differ in children with cystic fibrosis and non-cystic fibrosis bronchiectasis?

被引：0
作者：
Hulya Nilgun Gurses
Hikmet Ucgun
Melih Zeren
Hilal Denizoglu Kulli
Erkan Cakır
机构：
[1] Bezmialem Vakıf University,Division of Physiotherapy and Rehabilitation, Faculty of Health Sciences
[2] Bezmialem Vakıf University,Department of Cardiopulmonary Physiotherapy and Rehabilitation, Division of Physiotherapy and Rehabilitation, Faculty of Health Sciences
[3] Biruni University,Division of Physiotherapy and Rehabilitation, Faculty of Health Sciences
[4] Izmir Bakircay University,Division of Physiotherapy and Rehabilitation, Faculty of Health Sciences
[5] Istanbul Atlas University,Division of Physiotherapy and Rehabilitation, Faculty of Health Sciences
[6] Bezmialem Vakif University,Department of Pediatric Pulmonology, Faculty of Medicine
来源：
European Journal of Pediatrics | 2022年 / 181卷
关键词：
Cystic fibrosis; Non-cystic fibrosis bronchiectasis; Respiratory physiotherapy; Pulmonary function; Exercise capacity; Respiratory and peripheral muscle strength;
D O I：
暂无
中图分类号：
学科分类号：
摘要：
Bronchiectasis is a form of airway damage as a consequence of endobronchial infection and inflammation and may be present in different diseases. The underlying aetiologies include both cystic fibrosis (CF) and a group of non-cystic fibrosis diseases (NCFB) such as immunodeficiency, primary ciliary dyskinesia, or severe pulmonary infection. Although children with CF and non-cystic fibrosis bronchiectasis (NCFB) have many similar clinical features, their responses to exercise may be different. The aim of this study was to compare the efficacy of a comprehensive respiratory physiotherapy (CRP) home-program in children with CF and NCFB. Thirty children with CF and thirty children with NCFB were included in the study. Both groups performed the CRP home-program twice daily for 8 weeks. Pulmonary function, exercise capacity, and respiratory and peripheral muscle strength were assessed at baseline and after 8 weeks of training. Both groups experienced significant improvements in pulmonary function, exercise capacity, and respiratory and peripheral muscle strength (p < 0.001). Maximum expiratory pressure, exercise capacity, and peripheral muscle strength were further improved in NCFB group compared to CF (p < 0.05); however, there was a great variability in the improvements for each variable.
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页码：2961 / 2970
页数：9
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