Tubulopathy and hepatomegaly in a 2-year-old boy: Answers

被引:0
作者
Pembe Soylu Ustkoyuncu
Funda Bastug
Aslıhan Kiraz
Murat Erdogan
Esra Eren
Gokce Yıldız
机构
[1] Kayseri City Hospital,Pediatric Nutrition and Metabolism Clinic
[2] Kayseri City Hospital,Pediatric Nephrology Clinic
[3] Kayseri City Hospital,Genetic Clinic
[4] Kayseri City Hospital,Pediatric Gastroenterology, Hepatology and Nutrition Clinic
[5] Kayseri City Hospital,Pediatrics Clinic
来源
Pediatric Nephrology | 2021年 / 36卷
关键词
Child; Fasting hypoglycemia; Postprandial hyperglycemia; Hepatomegaly; Aminoaciduria; Fanconi-Bickel syndrome; mutation;
D O I
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中图分类号
学科分类号
摘要
引用
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页码:2083 / 2084
页数:1
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[1]  
Fanconi G(1949)Chronic aminoaciduria (amino acid diabetes or nephrotic-glucosuric dwarfism) in glycogen storage and cystine disease Helv Paediatr Acta 4 359-396
[2]  
Bickel H(2012)Fanconi-Bickel syndrome: GLUT2 mutations associated with a mild phenotype Mol Genet Metab 105 433-437
[3]  
Grünert SC(2015)Phenotypic variability in patients with Fanconi-Bickel syndrome with identical mutations JIMD Rep 15 95-104
[4]  
Schwab KO(2002)The mutation spectrum of the facilitative glucose transporter gene SLC2A2 (GLUT2) in patients with Fanconi-Bickel syndrome Hum Genet 110 21-29
[5]  
Pohl M(2017)A Fanconi-Bickel syndrome patient with a novel mutation and accompanying situs inversus totalis Turk J Pediatr 59 693-695
[6]  
Sass JO(2013)An Indian girl with Fanconi-Bickel syndrome without SLC2A2 gene mutation J Pediatr Genet 2 109-112
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