Excitation-induced ataxin-3 aggregation in neurons from patients with Machado–Joseph disease

被引：0

作者：

Philipp Koch

Peter Breuer

Michael Peitz

Johannes Jungverdorben

Jaideep Kesavan

Daniel Poppe

Jonas Doerr

Julia Ladewig

Jerome Mertens

Thomas Tüting

Per Hoffmann

Thomas Klockgether

Bernd O. Evert

Ullrich Wüllner

Oliver Brüstle

机构：

[1] Institute of Reconstructive Neurobiology,Department of Neurology

[2] Life and Brain Center,Department of Dermatology

[3] University of Bonn and Hertie Foundation,Institute of Human Genetics and Department of Genomics

[4] University of Bonn Medical Center,undefined

[5] 53105 Bonn,undefined

[6] Germany,undefined

[7] University of Bonn Medical Center,undefined

[8] 53127 Bonn,undefined

[9] Germany,undefined

[10] Life and Brain Center,undefined

[11] University of Bonn,undefined

[12] 53127 Bonn,undefined

[13] Germany,undefined

[14] DZNE,undefined

[15] German Center for Neurodegenerative Diseases,undefined

[16] 53175 Bonn,undefined

[17] Germany,undefined

来源：

Nature | 2011年 / 480卷

关键词：

D O I：

暂无

中图分类号：

学科分类号：

摘要：

Human neurons derived from induced pluripotent stem cells permit the study of aberrant protein processing and aggregation in Machado–Joseph disease.

引用

页码：543 / 546

页数：3

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