Excitation-induced ataxin-3 aggregation in neurons from patients with Machado–Joseph disease

被引：0
|
作者：
Philipp Koch
Peter Breuer
Michael Peitz
Johannes Jungverdorben
Jaideep Kesavan
Daniel Poppe
Jonas Doerr
Julia Ladewig
Jerome Mertens
Thomas Tüting
Per Hoffmann
Thomas Klockgether
Bernd O. Evert
Ullrich Wüllner
Oliver Brüstle
机构：
[1] Institute of Reconstructive Neurobiology,Department of Neurology
[2] Life and Brain Center,Department of Dermatology
[3] University of Bonn and Hertie Foundation,Institute of Human Genetics and Department of Genomics
[4] University of Bonn Medical Center,undefined
[5] 53105 Bonn,undefined
[6] Germany,undefined
[7] University of Bonn Medical Center,undefined
[8] 53127 Bonn,undefined
[9] Germany,undefined
[10] Life and Brain Center,undefined
[11] University of Bonn,undefined
[12] 53127 Bonn,undefined
[13] Germany,undefined
[14] DZNE,undefined
[15] German Center for Neurodegenerative Diseases,undefined
[16] 53175 Bonn,undefined
[17] Germany,undefined
来源：
Nature | 2011年 / 480卷
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摘要：
Human neurons derived from induced pluripotent stem cells permit the study of aberrant protein processing and aggregation in Machado–Joseph disease.
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收藏
页码：543 / 546
页数：3
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