Management of general anesthesia in a child with Miller–Dieker syndrome: a case report

被引：0
作者：
Chiaki Wakiguchi
Kohei Godai
Keika Mukaihara
Tetsuya Ohnou
Tamotsu Kuniyoshi
Mina Masuda
Yuichi Kanmura
机构：
[1] Graduate School of Medical and Dental Sciences,Department of Anesthesiology and Critical Care Medicine
[2] Kagoshima University,undefined
来源：
JA Clinical Reports | / 1卷 / 1期
关键词：
Miller–Dieker syndrome; Lissencephaly; Bispectral Index;
D O I：
10.1186/s40981-015-0017-2
中图分类号：
学科分类号：
摘要：
Miller–Dieker syndrome (MDS) is a rare disorder characterized by type I lissencephaly and a distinctive facial appearance that may include prominent forehead, bitemporal hollowing, and micrognathia. MDS is associated with epilepsy. We here report an 18-month-old girl with MDS who required general anesthesia. The child had an extremely low Bispectral Index (BIS) value prior to undergoing general anesthesia. Her perioperative course was uneventful. This case highlights some of the important anesthetic concerns in patients with MDS, which include potentially difficult airways and extremely low BIS values.
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