Impact of Surgery on Extramammary Paget’s Disease Vulva: a Case Series

被引：0
作者：
J. S. Anjana
P. Rema
S. Suchetha
J. Siva Ranjith
Amrita B. Rao
T. R. Preethi
机构：
[1] Regional Cancer Centre,Division of Gynecological Oncology
[2] Regional Cancer Centre,Division of Surgical Oncology
[3] Regional Cancer Centre,Plastic and Reconstructive Surgery
[4] Regional Cancer Centre,Department of Pathology
来源：
Indian Journal of Surgical Oncology | 2021年 / 12卷
关键词：
Surgery; Paget’s disease vulva; Hyperkeratosis;
D O I：
暂无
中图分类号：
学科分类号：
摘要：
Extramammary Paget’s disease is a rare neoplasm that may affect the vulva. It usually presents as a pruritic red eczematous lesion with islands of hyperkeratosis that is often mistaken for other benign conditions. There are no specific guidelines for the management of this disease. Surgical excision is the standard treatment but recurrences are common in spite of extensive surgery with negative margins. We report here a series of 7 cases of Paget’s disease vulva treated by primary surgery. The series highlights some of the challenges in the diagnosis and management of Paget’s disease vulva.
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页码：524 / 529
页数：5
相关论文
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