Acinar cell carcinoma of the pancreas

被引:31
作者
Rachel Pimenta Riechelmann
Paulo Marcelo Hoff
Renato Alonso Moron
Luiz Heraldo da Câmera Lopes
Antonio Carlos Buzaid
机构
[1] Albert Einstein Jewish Hospital,Department of Radiology
[2] M. D. Anderson Cancer Center,Department of Gastrointestinal Oncology
[3] Hospital Sirian Liban’s,Department of Pathology
[4] Hospital Sirian Liban’s,Department of Oncology
[5] Albert Einstein Jewish Hospital,Department of Oncology
来源
International Journal of Gastrointestinal Cancer | 2003年 / 34卷 / 2-3期
关键词
Acinar cell carcinoma; pancreas neoplasm; pancreatic cancer; paclitaxel; chemotherapy;
D O I
10.1385/IJGC:34:2-3:067
中图分类号
学科分类号
摘要
Acinar cell carcinoma of the pancreas is a rare tumor for which the best chemotherapy regimen has not been clearly established. Here, we report on a female patient with an unusually long survival and a remarkable response to weekly paclitaxel. To our knowledge, this is the first time that paclitaxel has been associated with an objective response in this disease. The patient recurred after initial resection and failed multiple prior chemotherapeutic regimens. She received weekly paclitaxel at 80 mg/m2 and responded after eight doses, maintaining controlled disease for a total of 4 mo. We present her case in detail and review the available literature regarding this rare type of tumor.
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页码:67 / 72
页数:5
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