Idiopathic Non-cirrhotic Portal Hypertension and Close Entities: a Need for Clarifying Terminology

被引：0

作者：

Andrea De Gottardi

Pierre-Emmanuel Rautou

机构：

[1] Hepatology, University Clinic of Visceral Surgery and Medicine, Inselspital Freiburgstrasse 18, Bern

[2] Department of Clinical Research, University of Bern, Bern

[3] Inserm, U970, Paris Cardiovascular Research Center—PARCC, Université Paris Descartes, Sorbonne Paris Cité, Paris

[4] DHU Unity, Pôle des Maladies de l’Appareil Digestif, Service d’Hépatologie, Centre de Référence des Maladies Vasculaires du Foie, Hôpital Beaujon, AP-HP, Clichy

来源：

Current Hepatology Reports | 2017年 / 16卷 / 3期

关键词：

Hepato-portal sclerosis; Incomplete septal fibrosis; Nodular regenerative hyperplasia; Obliterative portal veinopathy; Vascular liver disease;

D O I：

10.1007/s11901-017-0358-6

中图分类号：

学科分类号：

摘要：

Purpose of Review: Idiopathic non-cirrhotic portal hypertension is described with a very heterogeneous terminology depending on the geographic origin of the patients and on the possible underlying causes of the disease. We aim here to review the current nomenclature and to the pathophysiological origins of this entity. Recent Findings: In the past, a relevant number of definitions of this condition have been used in the literature, suggesting the presence of several distinct diseases. However, recent findings strongly suggest that there are some common denominators for this disease. Therefore, efforts should be made to develop a unified terminology encompassing the very essential features from clinical, histologic, imaging, laboratory and elastographic data. Summary: These findings suggest that the common localization of the disease is the portal and the sinusoidal compartment of the liver; therefore, a novel definition should be elaborated. © Springer Science+Business Media, LLC 2017.

引用

页码：237 / 240

页数：3

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